Uw0rLd 12/16/14

Question 1

Form of Congenital Adrenal Hyperplasia (CAH) that causes salt wasting and ambiguous genitalia in girls / precocious puberty in boys.

Answer 1

21-hydroxylase deficiency

Question 2

Which type of CAH is the most common?

Answer 2

21-hydroxylase deficiency

Question 3

What does “salt-wasting” mean?

Answer 3

low Na+, high K+, dehydration

Question 4

Which type of CAH will cause all pts to be phenotypically female and cause fluid retention?

Answer 4

17α-hydroxylase deficiency

Question 5

Which type of CAH causes salt/fluid retention and ambiguous genitalia in girls?

Answer 5

11β-hydroxylase deficiency

Question 6

Old guy w/ proximal muscle weakness and high CPK

Answer 6

dermatomyositis or polymyositis

Question 7

Addison’s disease will cause _______-kalemia.

Answer 7

hyper

Question 8

what steroid is used to tx addisonian crisis?

Answer 8

hydrocortisone

Question 9

what steroid is used to tx stable addison’s dz?

Answer 9

prednisone

Question 10

which steroid is used to tx hypotension in addison’s dz unresponsive to prednisone? why?

Answer 10

fludrocortisone; most mineralocorticoid activity

Question 11

hypertension + low K+ + low renin

Answer 11

hyperaldosteronism

Question 12

Tx for hyperaldosteronism caused by adrenal adenoma?

Answer 12

surgical resection

Question 13

Tx for hyperaldo caused by adrenal hyperplasia?

Answer 13

spironolactone

Question 14

what is the first step in mgmt of pheo?

Answer 14

phenoxybenzamine to control BP

Question 15

what is the second step after adding phenoxybenzamine for Tx of pheo?

Answer 15

propranolol

Question 16

pt w/ UTI has cultures (+) for proteud. she should be evaluated for _______.

Answer 16

kidney stones