Pulmonary 4

Question 1

CT appearance of PLCH

Answer 1

Diffuse, small cysts and centrilobular micronodules

Question 2

CT appearance of DIP

Answer 2

Nodules of various sizes on a background of ground glass opacities

Question 3

Most common form of ILD in Sjögren’s syndrome

Answer 3

NSIP

Question 4

Treatment of choice for pulmonary AVMs, especially when the feeding artery is >2-3 mm

Answer 4

Embolization

Question 5

Typical treatment for clinically significant radiation-induced lung injury (RILI)

Answer 5

1 mg/kg/ day prednisone x 2-4 wks; then slow taper over 7-12 wks

Question 6

Primary treatment for PLCH

Answer 6

Smoking cessation

Question 7

1st line Tx for LAM (w/ FEV1 <70% predicted)

Answer 7

Sirolimus

Question 8

_____ is a cystic lung disease that occurs in middle-aged women (incidence is twice that of men) with underlying autoimmune disease or immunodeficiency, most commonly Sjögren syndrome.

Answer 8

LIP

Question 9

uncommon condition characterized by dilatation of the trachea and major bronchi, with normal-diameter peripheral airways

Answer 9

Mounier-Kuhn syndrome (tracheobronchomegaly)