Diffuse Parenchymal Lung Disease 1

Question 1

TERT and TERC gene mutations are associated with

Answer 1

familial pulmonary fibrosis

Question 2

Rare disorder w/ hyperpigmented skin, oral leukoplakia, premature graying, and nail dystrophy

Answer 2

dyskeratosis congenita

Question 3

FLCN gene mutation

Answer 3

Birt-Hogg-Dubé syndrome

Question 4

Allodynia, hyperalgesia, or reduced pinprick or thermal sensation in sarcoidosis

Answer 4

small fiber neuropathy

Question 5

test to differentiate parenchymal from chest wall / neuromuscular causes of restriction

Answer 5

pressure-volume study

Question 6

What pressure is measured in a pressure-volume study?

Answer 6

esophageal pressure (estimate of pleural pressure)

Question 7

type of lung disease induced by daptomycin

Answer 7

acute eosinophilic pneumonia

Question 8

Which causes peripheral eosinophilia, acute or chronic eosinophilic pneumonia?

Answer 8

chronic

Question 9

Define peripheral eosinophilia for chronic eosinophilic pneumonia

Answer 9

> 500

Question 10

In acute eosinophilic PNA, eos are >___% of cells in BAL.

Answer 10

25%