Diffuse Parenchymal Lung Disease 3 Flashcards
1
Q
Cystic lung disease that stains for HMB-45
A
LAM
2
Q
Cystic lung disease that stains for S-100
A
PLCH
3
Q
Cystic lung disease that stains for CD1a
A
PLCH
4
Q
multiple, bizarre-shaped cysts and nodules, with a subtle mid to upper zone predominance, and interstitial thickening
A
PLCH
5
Q
Cysts of variable size and irregular shape, primarily in medial basilar lung zones
A
Birt-Hogg-Dubé
6
Q
Birt-Hogg-Dubé triad: cystic lung disease + _____ + _____
A
skin lesions; renal tumors
7
Q
fibrotic and cystic lung disease associated with autoimmune diseases (Sjogren’s, SLE)
A
LIP
8
Q
Tx for pts homo- or heterozygous for ΔF508 deletion
A
triple modulator Tx (Elexacaftor/Tezacaftor/Ivacaftor)
9
Q
anti-GM-CSF Ab
A
PAP
10
Q
How does anti-GM-CSF cause PAP?
A
macrophages aren’t produced, so they don’t clear alveoli
