Peutz-Jeghers Syndrome Flashcards
1
Q
What is peutz-Jeghers syndrome?
A
Autosomal dominant condition characterized by hamartomatous GI polyps and mucocutaneous hyperpigmentation
2
Q
What do patients with this condition have 15x the risk of developing?
A
Intestinal cancer
3
Q
Associated complications?
A
Bowel obstruction
Intussesception
4
Q
What is intussesception?
A
5
Q
Management of this?
A
Active cancer surveillance
