Peds Cardiac Flashcards
congenital heart dz –> CXR –> eval which structures? (2)
- pulm vasculature
- heart size
congenital heart dz –> CXR –> eval pulm vasc –> 3 types?
- increased pulm venous flow
- increased arterial flow
- decreased arterial flow
congenital heart dz –> CXR –> pulm vasc –> increased pulm venous flow –> imaging appearance?
peripheral 1/3 –> indistinct vessels & septal markings
congenital heart dz –> CXR –> pulm vasc –> increased pulm venous flow –> can be seen in what conditions? (4)
- hypoplastic L heart
- aortic coarctation
- congestive heart failure
- neonatal sepsis
congenital heart dz –> CXR –> pulm vasc –> increased arterial flow –> imaging appearance?
peripheral 1/3 –> distinct lrg-caliber vessels
congenital heart dz –> CXR –> pulm vasc –> increased pulm arterial flow –> can be seen in what conditions? (4)
L-to-R shunt:
- atrial septal defect
- VSD
- patent ductus arteriosus
- endocardial cushion defect (AV canal defect)
congenital heart dz –> CXR –> pulm vasc –> decreased arterial flow –> imaging appearance?
peripheral 1/3 –> decreased vasculature
congenital heart dz –> CXR –> pulm vasc –> decreased pulm arterial flow –> can be seen in what conditions? (2)
RV outflow tract insuff:
- Tetralogy of Fallot
- Ebstein anomaly
increased pulm venous flow –> aka?
pulm edema
extra-cardiac AV shunt –> 2 examples? (2)
- vein of Galen malformation
- infantile hepatic hemangioma
neonatal CHF –> etiology? (2)
- primary cardiac anomaly
- extra-cardiac arteriovenous shunt
endocardial cushion defect (AV canal defect) –> assoc synd? (1)
Down synd
congenital heart dz:
- increased pulm venous flow
- increased arterial flow
- decreased arterial flow
cyanotic vs acyanotic?
- increased pulm venous flow: acyanotic
- increased arterial flow: acyantoic
- decreased arterial flow: cyantoic
congenital heart disease:
- decreased pulm vasc
- cardiomeg
what condition? (2)
- Ebstein anomaly
- pulm atresia w intact septum
congenital heart disease:
- decreased pulm vasc
- normal heart size
what condition?
Tetralogy of Fallot
congenital heart disease:
- increased pulm vasc
- normal heart size
what condition? (5)
5 Ts:
- transposition of great arteries
- truncus arteriosus
- tricuspid atresia
- total anomalous pulm venous return (TAPVR)
- single ventricle
hypoplastic L heart –> spectrum of anomalies –> which L heart struct can be involved? (5)
- LA
- LV
- mitral valve
- aortic valve
- aorta
hypoplastic L heart –> fatal –> unless have what condition?
R-to-L shunt:
- patent ductus arteriosus
- ASD
- patent foramen ovale
what is ductus arteriosus? natural progression after birth?
short connection bw proximal left pulmonary artery and aortic arch –> blood bypass the non-ventilated lungs in the fetus
after birth –> decrease prostaglandins & decrease pulm art pressure –> ductus close 2 days after birth –> blood into pulm vasculature –> ligamentum arteriosum
hypoplastic L heart –> tx?
Norwood procedure
what is Blalock-Taussig shunt?
graft –> connect R subclavian A –> R pulm A
what is bidirectional Glenn shunt?
SVC connect to R pulm A
what is modified Fontan?
tunneled conduit –> connect IVC –> pulm A
neonatal CHF –> 2 MCC?
- vein of Galen malformation
- hepatic hemangioendothelioma
ASD –> RtoL or LtoR shunt?
L-to-R
ASD –> when present?
later childhood - early adult
ASD –> assoc condition? (1)
Holt-Oram synd
Holt-Oram synd –> synd? (2)
- ASD
- UE bone deformity (ie absence/hypoplasia thumb)
ASD –> MC type? MOA?
ostium secundum
septum secundum –> incompletely cover ostium secundum
ASD –> 2nd MC type? MOA?
ostium primum
septum primum –> incompletely fuse to endocardial cushion
sinus venosus ASD –> assoc condition?
anomalous pulm venous drainage
ASD –> what structure(s) is enlarged?
RA –> RV –> pulm A
VSD –> when present?
1mo
VSD –> 2 types of location?
- # 1 membranous
- muscular IV septum
VSD –> possible complication?
Eisenmenger synd
what is Eisenmenger synd?
pulm HTN –> reversal of shunt direction
VSD –> R or L heart is enlarged?
L
PDA –> classic clinical presentation?
premature –> 7-10 days of life –> CXR show CHF
endocardial cushion defect –> spectrum of anomalies –> such as? (4)
- ostium primum ASD
- VSD
- mitral anomaly
- tricuspid anomaly
endocardial cushion defect –> assoc condition?
trisomy 21
what is Ebstein anomaly?
tricuspid valve –> severe malformation –> leaflets displaced apically –> obstruct pulm valve –> RV outflow tract obstruction –> atrialization of RV
Ebstein anomaly –> what concurrent condition 100%?
ASD
Ebstein anomaly –> CXR appearance?
- huge heart –> enlrg RA –> “box shape”
- decreased pulm vasc
CXR –> massive R atrial enlrg & decreased pulm vasc –> ddx? (2)
- Ebstein anomaly
- pulm atresia w intact ventricular septum
pulm atresia w intact ventricular septum –> what happens to…
- RA
- RV
- pulm valve
- RA: enlrg
- RV: hypoplasia
- pulm valve: atretic
pulm atresia w intact ventricular septum –> how get pulm blood flow?
L-to-R shunt must be present (ie PDA)
Tetralogy of Fallot –> 4 components?
- pulm valve stenosis –> RV outflow tract obstruction
- RV hypertrophy
- VSD
- aorta override VSD
what is pentalogy of Fallot?
tetralogy of fallot + ASD
pediatric –> MC cyanotic heart dz?
ToF
adult –> MC cyanotic heart dz?
ToF
Tetralogy of Fallot –> assoc synd? (3)
- DiGeorge synd
- VACTERL
- trisomy 21
DiGeorge synd –> synd? (3)
- ToF
- absent thymus
- absent parathyroid
Tetralogy of Fallot –> CXR appearance?
- normal size heart –> RV hypertrophy –> cardiac apex uplifted –> “boot shape”
- decreased pulm vasc
Tetralogy of Fallot –> 25% have what other condition?
R aortic arch
Tetralogy of Fallot –> severe form?
pulm atresia w VSD
Tetralogy of Fallot –> tx?
surg:
- close VSD
- open RV outflow obstruct
newborn –> MC cyanotic heart dz?
transposition of great A
what is transposition of great A?
- RV –> aorta
- LV –> pulm A
transposition of great A –> what is required for survival?
site for blood mixture –> ie ASD, VSD, PDA, LtoR shunt)
transposition of great A –> US findings? (2)
- aorta ant to heart
- great vessels exit heart in parallel (rather than cross)
transposition of great A –> classic CXR finding? actual typical appearance?
classic: heart & narrow mediastinum –> “egg on a string”
typical:
- slightly narrow mediastinum
- increased pulm vasc
transposition of great A –> why mediastinum narrow on CXR?
- parallel config of great vessels
- thymus involute d/t stress
- lack of main pulm bulge
transposition of great A –> tx?
Jatene procedure –> arterial switch
tricuspid atresia + small VSD –> CXR appearance?
- normal heart
- decreased pulm vasc
tricuspid atresia + lrgVSD –> CXR appearance?
- lrg heart
- increased pulm flow
MC congenital heart dz w right arch?
truncus arteriosus
what is truncus arteriosus?
single great art –> supplies:
- systemic
- pulm
- coronary
overrides a VSD
truncus arteriosus –> CXR appearance?
- cardiomeg
- narrow mediastinum
- pulm edema
what is total anomalous pulm venous return (TAPVR)?
pulm veins go to systemic venous circ instead of LA
TAPVR –> types? (4)
- supracardiac: L brachiocephalic V
- cardiac: coronary sinus or RA
- infracardiac: hepatic IVC/portal/hepatic V
- mixed: combo of above
TAPVR –> MC type?
supracardiac
supracardiac TAPVR –> classic CXR finding?
snowman sign
TAPVR –> typical CXR appearance?
- normal heart
- pulm edema
TAPVR –> what must be present for blood to reach L heart?
interatrial R-L comm –> ASD
aortic coarctation –> locations? (3)
- preductal
- periductal
- postductal
aortic coarctation –> when present?
- preductal
- periductal
- postductal
- preductal: infant
- periductal: teen-early adult
- postductal: teen-early adult
aortic coarctation –> assoc condition?
bicuspid aortic valve
aortic coarctation –> assoc synd?
Turner synd
aortic coarctation –> classic CXR finding in adult?
3 sign
tuberous sclerosis –> earliest sign in utero?
cardiac rhabdomyoma
MC cardiac tumor?
rhabdomyoma
pediatric cardiac tumors? (4)
- rhabdomyoma
- teratoma
- fibroma
- hemangioma
2nd MC cardiac tumor detected in utero?
teratoma
cardiac teratoma –> MC location?
root of pulm A & aorta
pericardial teratoma –> potential complication?
massive perinatal pericardial effusion
cardiac fibroma –> MC location?
IV septum
cardiac hemangioma –> potential complication?
massive pericardial effusion
asplenia –> type of heterotaxy?
R-sided isomerism
polysplenia –> type of heterotaxy?
L-sided isomerism
Kawasaki dz –> acute phase –> what conditions are seen? (2)
- myocarditis
- heart fail
Kawasaki dz –> subacute phase –> what conditions are seen? (2)
coronary A aneurysm –> thrombus
hypoplastic L heart –> CXR findings?
- normal heart or cardiomeg
- pulm edema
transposition of great arteries –> D vs L?
D:
- deoxy: RA –> RV –> aorta
- oxy: LA –> LV –> pulm A
L: (congenitally corrected)
- deoxy: RA –> LV –> pulm A
- oxy: LA –> RV –> aorta