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Question 1

this:________________…. is a strong clue for differentiating Kawasaki disease from scarlet fever
and toxic shock syndrome.

Answer 1

Fissuring of the lips|

Question 2

idiopathic thrombocytopenic purpura

(ITP). What is the most appropriate treatment?

Answer 2

Children with little-to-no symptoms can typically be managed with observation alone regardless of platelet count.

First line therapy:
Steroids, or if not tolerated: IV immune globulin

but then…. 2nd line
splenectomy, and, for
life-threatening bleeding, platelet transfusions, and

Question 3

Who children with thrombocytopenic purpura should you treat?

Answer 3

Children who have platelet counts < 20 x 10^9/L and
significant mucous membrane bleeding and those who have platelet counts < 10x10^9/L and
minor purpura

Question 4

Von Willebrand’s disease physiopathology in two words

Answer 4

platelet dysfunction.

Question 5

Von Willebrand's disease labs would show:
platelet count:
bleeding time:
PT:
PTT:
aPTT

Answer 5

platelet count: normal
bleeding time: prolonged
aPTT High
PT: normal
PTT: possibly,  slightly prolonged
lo alto es la B!!!! como VW

Question 6

Von Willebrand’s disease CxFx

Answer 6

mild to moderate and include easy bruising; bleeding from small skin cuts that may stop and start over hours; sometimes, increased menstrual bleeding;
and abnormal bleeding after surgical procedures (eg, tooth extraction, tonsillectomy).

Question 7

Von Willebrand’s disease Dx

Answer 7

low levels of VWF antigen and abnormal ristocetin cofactor activity

Question 8

Von Willebrand’s disease Tx

Answer 8

control of bleeding

replacement therapy (cryoprecipitate or
pasteurized intermediate-purity factor VIII concentrate) or desmopressin (DDAVP)

Question 9

The most common cause of proteinuria in children is:

Answer 9

Orthostatic proteinuria

… accounts for up to 60% of all cases of asymptomatic proteinuria reported in children, with an even higher incidence in adolescents.

Question 10

Scabies Tx

Answer 10

Prescribe permethrin (Elimite) 5%

Question 11

This signs confirms the diagnosis of scabies

Answer 11

The mite burrow

Question 12

The disappearance of a ventricular septal defect (VSD) murmur in a patient known to have a
large left-to-right shunt is most likely due to:

Answer 12

Development of significant pulmonary arterial hypertension.

Due to the Eisenmenger’s syndrome

Question 13

Which prophylactic antibiotic therapy would you use for a tooth extraction in a patient with a prosthetic heart valve?

Answer 13

amoxicillin.
allergy? azitro OR clynda
given 30-60 min before the procedure.