kef 30 pathiseis periferikou ns Flashcards

1
Q

ti einai i baleriani ekfilisi

A

ekflisisi twn nevraksonwn twn nevrikwn kitarwn

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2
Q

xaraktiristiki okseia/ipokseia nevropatheia

A

guillain barre

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3
Q

kinitikes nevropatheies

A

guillain barre(flegmwnwdi apomielinwtiki) ,porfiria diftheritida kai molivdo

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4
Q

aisthitikes nevropatheies

A

apo lepra ,sd(aksoniki nevropatheia),amiloeidwsi ,elleipsib12(aksoniki nevropatheia)

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5
Q

sti nevroapraksia exoume _ enw stin aksonotmisi exoume_

A

tmimatiki apomielinwsi pou nevrou logo piesis,,,,,,,aksoniki ekfilisi(se oliki fasi nevronotmisi)

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6
Q

poio nevro perna apo ton tarsiaio solina kai poies oi kiries diakladwseis tou

A

to knimiaio/…. esw kai eksw pelmatiaio ,

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7
Q

peroniaia miiki atrofia nosos cmt i klironimiki kinitiki kai aisthitiki nevropatheia(hmsn)

A

provlima stin mielini(gonidia pmp-22,po) epomenos apomielinwsi,atrofia sta katw akra podia pelargou kai koilopodia

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8
Q

oikogeneis amiloeidikes polinevropatheies

A

epodines paresthisies sta katw akra,apoleia mikrwn aisthitikwn nevrwn prwta (thermokrasias kai ponou),meta diataraxi se ola ta oidi periferikwn nevrwn,(diataraxes aftonomou,provlima sta gonidia amiloeidikwn prwteinwn: transthiretinis(ttr) ,apolipoprwteini a1,gkelsonini

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9
Q

33% twn asthenwn 1-4 vdomades prin tin gb emfanizoun loimwksi apo poia mikrovia einai?

A

kampilovaktiridio tis nistidos(diarroiko sindromo),cmv,ebv,mikoplasma tis pnevmonias,ipatitida,hiv

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10
Q

pathan vlavi guillain barre(okseia flegmwnwdis apomielinwtiki polirizonevropatheia)

A

diaxiti poliestiaki tmimatiki apomielinwsi se ola ta periferika nevra ,sto simeio tis apomielinwsis exoume lfegmonwdi diithisi apo lemfokitara kai sto telos aksoniki ekfilisi

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11
Q

simtwmata gb

A

okseia nevromiiki paralisi,aniousa proodeftiki miiki adinamia mexri ofthalmokinitikous ,apo ta katw akra mexri ton avxena,,katargisi tenwntiwn antanaklastikwn apo tis prwtes imeres, paraisthisies kai mialgies

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12
Q

ergastiriaka evrimata gb

A

leukomatokittarikos dixasmos so eny(avksimeno lefkwma,fisiologika kittara),se ilektrofisiologiko elegxo exoume meiomeni taxitita agwgis k F kimma se eksetaseis aimatos exoume: antiswmata kata gaggliosidwn GM1 (25% twn periptwsewn),tke,lefka,ipatika ,meiwsi na(provlima stin antidiouritiki)

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13
Q

klinikes parallages gb

A

sindomo miller fisher(ekswteriki ofthalmopligia ataksia kai katargisi tenontiwn antanaklastikwn) : ston oro IgG enanti gaggliosidiou GQ1b ,

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14
Q

poreia gb

A

egkatastasi 1-4 w
statheropoisi 2-4 w
apokatastasi 6m -2y

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15
Q

therapeia gb

A

plsamaferesi 2-4 siedries

iv anososfairini 0,4g/kg gia 5d

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16
Q

xronia flegmonwdis apomielinwtiki polirizonevropatheia CIDP ,poia einai ta ipoxrewtika klinika kritiria diagnwsis

A

proodeftiki miiki adinamia(>2 months)
meiwsi i katargisi antanaklastikwn
miiki adinamia kai periferika aisthitika simptwmata

17
Q

xronia flegmonwdis apomielinwtiki polirizonevropatheia,ergastiriaka (therapeia ;prednizoni kai plasmaferesi)

A

prwteini eny >45mg/ml kai kittara therapeia prednizoni

18
Q

poies nosoi kanoun paraprwteinemia(avksisi monoklwnikou antisomatos dld anososferines apo plasmatokitara)

A

mielwma,lemfwma,makrosfairinaimia ,sistimatiki amiloeidwsi,aftes oi paraprwteines Ig(M–>MAG,G,A) exoun antigona stoxous

19
Q

poreia makrosfairinaimias tou waldenstrom

A

kakoithi lemfokittara ston mielo ,ekrinoun igM monoklwniki prwteini , afti kanei vareia simmertriki aisthitiki nevropatheia (paraisthisies algos +krampes ,anti MAG drastiriotita

20
Q

prosvoli periferikou nevrikou ti exoume me poiu katastrofi

A

katastrofi kitarikou swmatos:nevrwnopatheia eite kinitiki(prwsthio keras) eitai aisthitiki(nwtiaio gagglio) ,..aksonikes nevropatheies vlavi stous nevraksones kinitikous i aisthitikous….apomielinwtikes nevropatheies elitro mielinis schwann–>parempidisi agwgimotitas miiki adinamia ipies diataraxes aisthitikotitas (meiwsi taxititas agwgis)…meiktes nevropatheies(aksoniki ekfilisi tmimatiki apomielinwsi)

21
Q

nevropatheies aksonikes

A

idiopathis,metabolikes :diavitiki ipothireoeidiki nefriki aneparkeia ,toksikes ,steritikes alkool b12 e, sistimatikes sarkoeidwsi likos ,paraprwteinaimikes paraneoplasmatikes

22
Q

nevropatheies apomielinwtikes

A

FLEGMONWDEIS gb cidp poliestiaki kinitiki nevropathiea paraprwteinaimikes KLIRONOMIKES cmt t1 kai tipou 2 TOKSIKES,MITOXONDRIAKES,LOIMWDEIS ,LEMFWMA

23
Q

polinevropatheia :

A

simmetriki prosvoli twn periferikwn nevrwn apo toksikes metavolikes i klironomikes astheneies….ekfrazete eitai periferikou tipou (ganti kaltsa ) eitai kentromielikou tipou

24
Q

ti mporei na kanei pagidevsi nevrou

A

ipothireieidismos ,akromegalia ,arthropatheies ,kai katastaseis me genikevmeno eidima

25
aisthitikokinitikes nevropatheies
sd ,nefriki aneparkeia alkoolismo ipith
26
aftonomes nevropatheies
diaviti + prwima stadia amiloeidwsis
27
sindromo karpiaiou solina logoi:(nevropatheia apo pagidevsi)
topiki pathologiki diergasia : travma ,lipwma kisti osteorthritikes alloiwseis ,se sxesi me sistimatikes katastaseis :egkimosini ipoth,akromegalia ,amiloeidwsi , idiopathes
28
kliniki eikona sindromo karpiaiou solina
ponos kai paresthisies 3 prwtwn daktilwn kai palamis,mporei na antanakla kai kentrikotera,ipoxoroun me kremasma kai tinagma xeriwn,miiki adinamia atrofia ipaisthisia
29
poio nevro kanei paraisthitiki miralgia
to eksw dermatiko nevro tou mirou
30
sindromo tarsaiou swlina
dialeiponta kavstika algi stis patouses, aimwdies ,ipaisthisia
31
avxeniki plegmatopatheia
prokaleitai apo ogkous pnevmona agkeiaka (s.d) toksika i aktinovolia,kanei pono ipaisthisia kai meiwsi kinitikotitas stin perioxi pou nevrwnei