Ehlers-Danlos Syndrome Flashcards
1
Q
What is ehlers-danlos syndrome?
A
Heterogeneous disorder of connective tissue
Affects structure, production or processing of collagen
2
Q
What are the hallmarks ehlers-danlos syndrome?
A
Tissue fragility
Joint hypermobility
Skin hyperextensibility
3
Q
What are the s/s of ehlers-danlos syndrome?
A
Joint hypermobility Skin atrophy/ velvety skin Medium and large vessel rupture Easily bruises Organ rupture Premature rupture of fetal membranes
4
Q
What are the treatment options of ehlers-danlos syndrome?
A
- Manifestations of the syndrome
- Care with suturing
- Prophylacitc β blocker to protect vessels
