Chapter 30

Question 1

Abnormally precipitated oxidized hemoglobin within an erythrocyte

Answer 1

Heinz body

Question 2

An endogenous inhibitor of coagulayion

Answer 2

Protein S

Question 3

Presence of immature nucleated red blood cells in the blood

Answer 3

Erythroblastosis

Question 4

Normal enzyme that protects erythrocytes from oxidative damage

Answer 4

G6PD

Question 5

Variations in hemoglobin levels between the sex is a rise during. ..and show … levels in healthy males

Answer 5

Adolescence, higher

Question 6

Iron deficiency anrmia in children is highest before age …

Answer 6

2

Question 7

Iron deficiencies anemia in children is due to…

Answer 7

Imbalance between dietary iron intake, the need for iron for normal growth, any occult blood loss

Question 8

A child who has a G6PD deficiency must not be given …

Answer 8

Aspirin

Question 9

Aspirin can trigger a … episode in children w a G6PD deficiency

Answer 9

Hemolytic

Question 10

Sickle cell disease is an autosomal…. condition

Answer 10

Recessive

Question 11

Sickle cell is expressed in the … form as sickle cell trait and in the … form as sickle cell disease

Answer 11

Heterozygous, homozygous

Question 12

Sickle cell anemia is often detected at … because fetal hemoglobin … affected by the genetic mutation

Answer 12

6-12 mnths, is not

Question 13

Von willerbrand disease is a genetic … condition

Answer 13

Hemorrhagic

Question 14

before the bone marrow is functional in a fetus production of erythrocytes take place primarily in the …and to a lesser extent in the spleen and lymph nodes

Answer 14

Liver

Question 15

A child who has sickle cell anemia and develops a parvovirus B19 infection may develop … crisis

Answer 15

Aplastic

Question 16

Acute chest syndrome in sickle cell anemia occurs when sickled erythrocytes cause … infarction

Answer 16

Lung

Question 17

Young children with sickle cell anemia may develop … crisis when large amounts of blood pool in the spleen and liver, potentially causing death from … …

Answer 17

Sequestration, cardiovascular collapse

Question 18

Beta-thalassemia major also is called … anemia

Answer 18

Cooley

Question 19

In cooley anemia the erythrocytes are unstable and prone to hemolysis because they have too many free hemoglobin … chains

Answer 19

Alpha

Question 20

Children with hemophilia experience recurrent episodes of …

Answer 20

Bleeding

Question 21

Children w hemphilia may develop limited mobility due to damage to … from some of there bleeding episodes

Answer 21

Joints

Question 22

the most common leukemia in children is

Answer 22

Acute lymphocytic leukemia ALL

Question 23

ALL causes……

Answer 23

Bone marrow failure with pallor, fatigue, purpura, bleeding, and fever

Question 24

Fever in acute leukemia is caused by … due to decreased neutrophils and by … from rapid growth of leukemic cells

Answer 24

Infection, hypermetabolism

Question 25

Children who have inherited deficiencies of antithrombin III or proteins C or S have increased risk for …..

Answer 25

Thrombosis

Question 26

Hodgkin lymphoma is characterized by …. enlargement of supraclavicular or cervical lymph nodes and has some association with …. …. virus

Answer 26

Lymphoid, epstein-barr

Question 27

Autosomal recessive factor xi deficiency

Answer 27

Hemophilia c

Question 28

X-linked recessive factor viii deficiency

Answer 28

Hemophilia a

Question 29

X-linked recessive factor ix deficiency

Answer 29

Hemophilia b