Cardio path1

Question 1

R to L shunts:

Answer 1

“early cyanosis, blue babies”

Tetralogy of Fallot
Transposition of great vessels
Trucus arteriosus (persistent)
Tricuspid atresia
Total anomalous pulm venous return (TAPVR)

Question 2

R to L shunts: truncus arteriosus (persistent)

Answer 2

Failure of truncus arteriosus to divide into pulm trunk and aorta; most pts have accompanying VSD.

Question 3

R to L shunts: tricuspid atresia

Answer 3

Absence of tricuspid valve and hypoplastic RV;

requires both ASD and VSD for viability

Question 4

R to L shunts: TAPVR

Answer 4

Pulm veins drain into right heart circulation (SVC, coronary sinus, etc), associated with ASD and soemtimes PDA to allow for right to left shunting to maintain CO

Question 5

L to R shunts:

Answer 5

“Late cyanosis, blue kids (vs. babies in R to L shunt)”

1) VSD (most common congenital cardiac abn)
2) ASD (loud S1, wide, fixed split S2)
3) PDA (close with indomethacin)

Frequency: VSD>ASD>PDA