16 NOV 2016 2102 PED Flashcards
what organism is the most common cause of sepsis in patients with sickle cell disease?
s. pneumo
hereditary spherocytosis is confirmed via what two blood tests?
- acidified glycerol lysis
- eosin-5-maleimide binding tests
what is Todd paralysis? how does it present?
- self-limited, focal weakness that occurs after a focal or generalized seizure
- presents as hemiplegia involving ipsilateral upper and lower extremity
in gonadotropin independent precocious puberty, what are the LH levels at baseline? what about after GnRH stimulation?
- low at baseline
- do not increase after GnRH stimulation
chronic overdose of vitamin A can lead to what condition?
increased intracranial pressure (pseudotumor cerebri)
doxycycline is contraindicated in children age ____ and younger
doxycycline is contraindicated under age 8 (and pregnant women)
patients with beckwith wiedman syndrome are predisposed to what two types of tumors? what is the workup?
- wilms tumor
- hepatoblastoma
- abdominal US and AFP levels every 3 months from birth to age 4
- abdominal US from 4-8
- renal US 8-adolescence
lead chelation therapy is not recommended or administered for lead levels under _____ ug/dL
45
what agent is used when lead levels are 45-69 ug/dL? what about over 70 (or acute encephalopathy)?
- 45-69: DMSA
- 70 / encephalopathy: dimercaprol plus EDTA
what is beck’s triad for pericarditis?
- distant heart sounds
- distended jugular veins
- hypotension
why do patients with selective IgA deficiency get anaphylaxis when given blood products?
they can develop IgE anti-IgA antibodies, and there are small amounts of IgA in blood products
what should be suspected in a patient with pancytopenia following drug intake, exposure to toxins, or viral infections?
acquired aplastic anemia
where do ewing sarcomas metastasize?
lung and lymph nodes
