Osteofibrous Dysplasia

Question 1

What is a rare form of fibrous dysplasia that primary affects the tibia and is confined to the cortices?

Answer 1

Osteofibrous dysplasia; also known as ossifying fibroma and Campanacci lesion

Question 2

How does an osteofibrous dysplastic lesion present?

Answer 2

Pain, anterior or anterolateral bowing in a young (<10yo) patient; 10-30% will present with a pseudoarthrosis

Question 3

What are the histiologic and radiographic characteristics of osteofibrous dysplasia?

Answer 3

Anterior cortical lesion of the tibia that leads to bowing; histologically similar to fibrous dysplasia except that it has osteoblastic rimming; most are treated with observation