Inherited Cardiac Channelopathies Flashcards
1
Q
two syndromes associated with congenital long QT syndrome
A
Romano-Ward syndrome
Lange-Nielsen syndrome
2
Q
hallmark of long QT syndrome
A
polymorphic VT (torsades de pointes)
3
Q
management of long QT syndrome
A
beta blockers
avoiding triggers e.g. swimming, breath holding and sudden loud noises
diet should be K+ rich
4
Q
define Brugada syndrome
A
risk of polymorphic VT or VF
5
Q
ECG of Brugada syndrome
A
ST elevation and RBBB in V1-V3
6
Q
management of Brugada syndrome
A
avoid excessive meals and alcohol
prompt fever medication
ICD if ventricular arrhythmias persist
7
Q
two examples of short QT syndrome
A
familial AF
WPW syndrome
