12/23/12 b

Question 1

Why should children w/ myocarditis be monitored in the ICU (2 most dangerous complications)?

Answer 1

acute decompensation, fatal arrhythmias

Question 2

A severe form of what condition is indicated by slowly developing back pain, neurologic dysfunction, and a palpable “step-off_ in the lumbosacral area?

Answer 2

spondylolisthesis

Question 3

What condition is indicated if a neonate presents with ambiguious genitalia, dehydration, low Na+, and high K+?

Answer 3

21-hydroxylase deficiency (complete)

Question 4

What are the manifestations of 3-β-hydroxysteroid dehydrogenase deficiency?

Answer 4

salt-wasting and ambiguious genitalia in either sex (hi DEAS, low testosterone)

Question 5

What are the manifestations of 11-β-hydroxylase deficiency?

Answer 5

hypertension, virilization

Question 6

What are the manifestations of 17-α-hydroxylase deficiency in both sexes?

Answer 6

hypertension, hypokalemia

Question 7

What is the result of 17-α-hydroxylase on genetic males?

Answer 7

pseudohermaphroditism (phenotypic female, no internal female sex organs d/t MIF)

Question 8

What is the result of 17-α-hydroxylase deficiency in genetic females?

Answer 8

phenotypically female, no secondary sex characteristics

Question 9

What is the most common form of CAH?

Answer 9

21-hydroxylase deficiency

Question 10

A 2-y.o. child should have a vocab. of approx. _______ words and should be able to make ___#___-word sentences. A stranger should be able to understand about (fraction) of what he says.

Answer 10

200; 2; half

Question 11

What skin disease occurs superimposed over healing atopic dermatitis with numerous umbilicated vesicles? Causatave agent?

Answer 11

eczema herpeticum; HSV

Question 12

What is the correct mgmt of a case of eczema herpeticum?

Answer 12

immediate acyclovir, as the condition may be life-threatening

Question 13

If you see a child with signs of congenital heart disease, fever, and focal neurologic deficits, what should you suspect?

Answer 13

brain abscess

Question 14

Pts w/ an epidural hematoma and signs of deteriorating neurological status should receive an emergent _______.

Answer 14

craniotomy

Question 15

What is post-pericardiotomy syndrome?

Answer 15

Reactive pericarditis in pts. who have had recent cardiac surgery. (pericardial effusion and tamponade,pleuritis, and pulm. effusion are complications.)