Witrak final buzzwords Flashcards
chronic pulmonary parenchymal disease
cor pulmonale
isolated RIGHT sided hypertensive heart disease
Most RV HF due to:
LV failure
primary adult cardiac tumor
atrial myxoma
primary child cardiac tumor
rhabdomyoma
if BNP
heart failure not likely
commonest acquired valvular disease in developed countries
Calcified aortic stenosis
congenital acceleration of aortic stenosis
bicuspid valve
systolic click
mitral valve prolapse
demographic for mild MV prolapse
young women
prosthetic heart valve infectious endocarditis (bug)
Staph epidermidis (coag negative)
sudden death in young athletes
hypertrophic cardiomyopathy
hemochromotosis
dilated (usually) cardiomyopathy
restrictive cardiomyopathy
CONGO RED positive
amyloidosis
USA- Coxackie B, adenovirus
Developing countries- Chagas disease
Myocarditis –> cardiomyopathy
ACUTE HF post-viral infx
common HF cause in children
myocarditis
most likely cause of FATAL tamponade
retrograde aortic dissection
ruptured AMI
penetrating chest wound
major causes of pericarditis in developing countries
HIV
TB
**developed countries- Coxackie, echo, EBV, CMV, influenza, varicella, rubella, HIV, hep B…
granulomatous pericarditis
TB
newborn cyanosis
right to left shunts
- tetralogy of fallot
- transposition of great arteries
- truncus arteriosis
left to right shunt reverses to right to left
Eisenmenger syndrome
Rx to keep ductus arteriosus patent:
PGE1
sudden cardiac death in adults
atherosclerotic CAD
cardiomyopathy
85%
sudden cardiac death in children
myocarditis
coronary artery anomalies
sudden cardiac death with negative forensic autopsy
think (3 things)
ion channel disorders:
long QT syndrome
Brugada syndrome
Catecholaminergic polymorphic V tach
commonest medium/large artery vascular disease
atherosclerosis
non-bypassable disease in microvasculature
arteriolosclerosis
***think HTN, DIABETES
Type A aortic dissection
ascending +/- distal aorta
Type B aortic dissection
descending and/or aortic arch
risks for aortic dissection
HTN
inherited CT disorder (ie. Marfan’s)
middle age/ elderly vasculitis
risk of vision loss
Temporal (Giant cell) arteritis
c-ANCA
anti-PR3
Wegner’s
anti-GBM
Goodpasture’s
asthma
anti-MPO (myeloperoxidase)
Churg-Strauss
DDx: pulmonary hemorrhage + glomerulonephritis
Wegner’s/ microscopic polyangiitis
Goodpasture’s
SLE
pANCA
microscopic polyangiitis
distal extremity arteritis in HEAVY SMOKERS
Buerger’s Disease
HHV-8 associated malignant vascular proliferation
Kaposi’s sarcoma
hyperplastic arteriolosclerosis
fibrinoid necrosis
lumen narrowing
malignant HTN (> 180 sys or 120 dias)
commonest cause of secondary HTN
renal disease
renovascular artery sclerosis in young-middle aged women
think:
fibromuscular dysplasia
“string of beads”
fibromuscular dysplasia
increased plasma aldosterone/renin ratio
Hypokalemia
secondary HTN
primary aldosteronism
paroxysmal HTN
HA
palpitations
diaphoresis
Pheochromocytoma
HTN
Turner syndrome
coarctation of the aorta
sequelae of chronic HTN
systemic atherosclerosis
thoracic aortic aneurysm
aortic dissection
magnifier of vascular morbidity
Diabetes
typical patients with Calciphylaxis
uremic (ESRD)
vasculitis in children
Kawasaki’s
Henoch-Schonlein purpura (HSP)
palpable purpura
vasculitis
hep B
polyarteritis nodosa
hypersensitivity vasculitis
HSP
drug related
cryoglobulinemic vasculitis
hep C
young women
aortic arch vasculitis
pulseless disease
granulomatous
Takayasu’s arteritis
polymyalgia rheumatica
Giant cell (temporal arteritis)
neutrophilic vasculitis
polyarteritis nodosa
Kawasaki’s mimics presentation of _________ in children
viral infx
Only reason to give ASA to kids?
Kawasaki’s
IgA deposition in patients
HSP
henoch schonlein purpura
potentially fatal venous varicosities
cirrhosis
esophageal varices