Scleroderma

Question 0

What is mauskauf a feature of?

Answer 0

All types of scleroderma

Question 1

What are the 3 different types of scleroderma and what alternate names may be used for them?

Answer 1

1) localized/ morphea
2) limited systemic/ crest syndrome
3) diffuse systemic/ generalized

Question 2

Explain the manifestations of localized scleroderma.

Answer 2

Localized- usually young onset, may stunt growth

• white or pink oval patches, bands, lines
• no blood manifestations

Question 3

What gender is more affected by scleroderma?

Answer 3

Women

Question 4

What does crest stand for?

Answer 4

Calcinosis- tiny calcium deposits
Raynaud’s
Esophageal dysmotility- poor function of lower 2/3 of esophagus. Heart burn, inflamm, dysphagia
Sclerodactyly- shiny puffy appearance
Telangiectasia- tiny red blotches from dilated capillaries

Question 5

With diffuse, one of the big problems is malignant hypertension or congestive heart failure.

T/F?

Answer 5

True. So this needs to be assumed on an OP even if it is not on the stem.

Question 6

Swallowing issues
Gerd
How would you modify for these? Which types would have this?

Answer 6

Put in side lying or semi reclined.

Question 7

What are the causes of scleroderma?

Answer 7

Idiopathic
Hereditary
Environment

Question 8

Name the manifestations of limited systemic sclerosis

Answer 8

Herald sign is Raynaud’s
Crest
Pulmonary hypertension
Other autoimmune disease possibly

Question 9

Name the manifestations of diffuse systemic sclerosis

Answer 9

Rapidly progressive, debilatating, renal and pulmonary involvement, skin lesions on trunk *** hallmark of this type, malignant hypertension and congestive heart failure, death within a few years
Abdominal issues- gas, constipation, diarrhea, etc