Restrictive Lung Diseases Flashcards

1
Q

characterized by a reduction in lung compliance or increased external pressures around the lungs limiting lung inflation during inhalation

A

restrictive lung disease

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2
Q

without correction of underlying processes, all restrictive lung diseases progress to: (4)

A

hypoxemia
pulmonary hypertension
cor pulmonale
respiratory failure

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3
Q

what would a spirometry look like for a patient with restrictive lung disease?

A

TLC decreased
FEV1 decreased
FVC decreased
FEV1/FVC ratio normal or increased

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4
Q

how would a restrictive lung disease flow loop look like?

A

normal but smaller
OR
moved to the right

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5
Q

restrictive lung disease that leads to sudden respiratory distress and could be caused by a sudden influx of fluid into alveolar spaces and parenchymal tissues

A

acute restrictive lung disease

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6
Q

restrictive lung disease with insidious onset with no initial symptoms

A

chronic

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7
Q

what is chronic restrictive lung disease also known as?

A

interstitial lung disease

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8
Q

a type of interstitial lung disease with unclear etiology

A

idiopathic interstitial pneumonia

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9
Q

a restrictive lung disease that results in diffuse lung scarring

A

idiopathic pulmonary fibrosis

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10
Q

a patient that presents with a dry cough, progressive dyspnea, and symptoms isolated to the lungs, is most likely experiencing what?

A

idiopathic pulmonary fibrosis

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11
Q

what are 4 diagnostics that can be used for IPF?

A

spirometry
chest xray
chest CT
lung biopsy

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12
Q

what would be seen in a chest xray of IPF?

A

reticular markings - “ground glass”

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13
Q

what would be seen in a chest CT of IPF? (2)

A

honey-comb
ground glass

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14
Q

what should be done for a patient with IPF?

A

referral to pulmonologist

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15
Q

what is the first step in treatment for IPF?

A

supplemental O2

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16
Q

what are 2 medications that can slow the progression of IPF?

A

nintedanib
pirfenidone

17
Q

what is the only definitive treatment of IPF?

A

lung transplant

18
Q

an inflammatory change characterized by noncaseating granulomas and is a multisystem disorder

A

sarcoidosis

19
Q

a patient presents with fatigue, fever, night sweats, weight loss, dry cough, dyspnea, crackles/rales on exam, lupus pernio, erythematic nodules, maculopapular trunk lesions, dry eyes, granules in lymph nodes and liver, anemia, splenomegaly, hypercalcemia, and decreased PTH. what is this patient likely experiencing?

A

sarcoidosis

20
Q

why does sarcoidosis cause hypercalcemia?

A

granulomas produce vitamin D

21
Q

what would be seen in a CXR for sarcoidosis?

A

bilateral hilar adenopathy

22
Q

what would be found in labs for sarcoidosis? (4)

A

leukopenia
elevated ESR
hypercalcemia
low PTH

23
Q

why would we do a biopsy for sarcoidosis?

A

rule out malignancy and infection

24
Q

what should be done for a patient with sarcoidosis?

A

referral to pulmonolgy

25
Q

what is the first line treatment for sarcoidosis?

A

long-term prednisone

26
Q

what is the 2nd line medication for refractory sarcoidosis?

A

methotrexate