PEDIATRICS Section 5: CHEST (PRIMARY lung Tumors)

Question 1

Developmental/congenital lung lesions will present at wide trimester?

Answer 1

Mid-second trimester US

Question 2

Normal 2nd trimester USD + Infant with lung tumor

Answer 2

Primary Lung tumor

Question 3

This is the most common primary lung malignancy in children

Answer 3

Pleuropulmonary Blastoma (PPB)

Question 4

what is the difference between CCAP and Pleuropulmonary Blastoma?

Answer 4

They can look a
lot like CCAMs and even have different types (cystic, mixed, solid) - but should be absent on the second trimester US.

Question 5

What is the difference between Pleuropulmonary Blastoma (PBB) and Askin/Ewings sarcoma in the chest wall?

Answer 5

NO RIB invasion

Question 6

This is the most cormnon primary lung mass in children.

Answer 6

Inflammatory Myofibroblastic Tumor (IMT)

Question 7

Describe Inflammatory Myofibroblastic Tumor (IMT)

Answer 7

These are solid masses, typically lobulated and
often calcified. They have a lower lobe predominance. The tend to look like fluid on MR (T2 bright) because they are composed of “myxoid” stroma.

It can look like a sequestration (given the arterial supply) or the solid types of PPB.