PEDIATRIC Section 7: Luminal GI (SPECIAL TOPICS) Flashcards

1
Q

Extra-abominal evisceration of neonatal bowel (sometimes stomach and liver) through a paraumbilical wall defect.

A

Gastroschisis

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2
Q

Herniated bowel loop through the ventral body wall NOT surrounded by a membrane

A

Gastroschisis

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3
Q

Herniated bowel loop through the ventral body wall Surrounded by a membrane (peritoneum)

A

Omphalocele

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4
Q

Herniated bowel loop through the ventral body wall + Normal Umbilicus - poistioned to the left of the defect (Defect is on the right)

A

Gastroschisis

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5
Q

Herniated bowel loop through the ventral body wall + Umbilicus contains hemiated bowel, and therefore is NOT normal

A

Omphalocele

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6
Q

Herniated bowel loop through the ventral body wall + Defect is on the right

A

Gastroschisis

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7
Q

Herniated bowel loop through the ventral body wall + Defect is midline

A

Omphalocele

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8
Q

Herniated bowel loop through the ventral body wall + with rare associated anomalies

A

Gastroschisis

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9
Q

Herniated bowel loop through the ventral body wall + High Association with Cardiac (50%) defects and Chromosomal Abnormalities

A

Omphalocele

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10
Q

What associated anomalies are common in omphalocele?

A

Trisomy 18
Turners
Klinefelters
Beckwith-Wiedemann,
Pentalogy of Cantral

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11
Q

Herniated bowel loop through the ventral body wall + good outcome

A

Gastroschisis

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12
Q

Herniated bowel loop through the ventral body wall + Intenstinal atresias

A

Gastroschesis

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13
Q

Herniated bowel loop through the ventral body wall + Cause: environmental

A

Gastroschesis

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14
Q

Herniated bowel loop through the ventral body wall + Genetic

A

Omphalocele

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15
Q

What is Pentalogy of Cantrell

A
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16
Q

What is an Enteric Duplication cyst?

A

developmental anomalies (failure to canalize)
DONT have comminication with GI lumen

17
Q

Where are enteric duplication cysts commonly found?

A

Ileal region (40%)

18
Q

Enteric Duplication cysts can cause what condition?

A

In Utero Bowel obstriuction/Perforation

19
Q

Diagnosis?

A

Enteric Duplication Cyst

20
Q

If you have a random cyst in the abdomen you need to ask yourself what?

A

“does this have gut signature? ”

21
Q

WTF is gut signature?

A

It’s alternating bands of hyper and hypo echoic signal - supposedly representing different layers of bowel.

22
Q

Cyst wih Gut Signature =

A

Enteric Duplication Cyst

23
Q

Cyst without Gut signature

A

Omental Cyst

24
Q

30% of the time, Enteric Duplication cysts are associated with what anomalies?

A

Vertebral anomalies

25
Q

This is a cause of bowel obstruction in an older kid (20 year old) with cystic fibrosis (CF)

A

DIstal Intestinal Obstruction Syndrome

26
Q

This is sometimes called the “meconium ileus equivalent, ” why?

A

DIstal Intestinal Obstruction Syndrome

because you end up with a distal obstruction (as the name implies) secondary to dried up thick stool.

27
Q

DIstal Intestinal Obstruction Syndrome commonly involves what part of the colon?

A

Ileum/right colon

28
Q

Self-limiting, usually viral inflammatory condition o f mesenteric lymph nodes. It is a classic clinical mimic of appendicitis.

A

Mesenteric Adenitis

29
Q

cluster of large right lower quadrant Ivmph nodes.

A

Mesenteric Adenitis

30
Q

immature bowel mucosa (from being premature or having a heart problem), and you get translocated bugs through this immature bowel.

It’s best thought o f as a combination o f ischemic and infective pathology.

A

Necrotising Enterocolitis (NEC)

31
Q

Necrotising Enterocolitis (NEC)!

Who gets it?

A
  • Premature Kids (90% within the first 10 days of life)
  • Low Birth Weight Kids ( < 1500 grams)
  • Cardiac Patients (sometimes occult) - they can be full term
  • Kids who had perinatal asphyxia
  • Hirschsprung Kids that go home and come back - they present around month 1.
32
Q

most definitive finding of NEC

What do you look for?

A

Pneumatosis

Look for Portal Venous Gas Next

33
Q

the region most affected by NEC

A

terminal ileum / right colon - Focal dilated bowel

34
Q

Describe the small bowel in NEC

A

Featureless small bowel, with separation (suggesting edema).