Pediatric Pathology Flashcards
Primary errors of morphogenesis
Intrinsic disturbance
Malformations
Anencephaly
Arnold chiari
Types of congenital anomalies
Malformations Disruptions Deformations Sequences Syndromes
Secondary destruction of a prev normal structure
Extrinsic disturbance
Disruption
Amniotic bands
Compression usually by uterine constraint
Deformations
Club foot
Cascade of anomalies by one initiating aberration
Sequences
Potter
Constellation of congenital anomalies
Syndrome
Congenital rubella
Disorders of prematurity
HMD
Nec enterocolitis
Pneumatosis intestinalis
Nec enterocolitis
Erythroblastosis fetalis
Large chorionic villi
Bilirubin at basal ganglia
Kernicterus
Immune hydrops
RhIg to Rh negative mothrs
28 weeks AOG, within 72 h of delivery or following abortions
Non immune hydrops causes
Parvovirus B19
Cardiac, anemia
Chromosomal
Twin twin transfusion syndrome
Inborn errors of metabolism
PKU
Galactosemia
Cystic Fibrosis
MCC death in cystic fibrosis
P aeruginosa
MC finding in SIDS
Multiple petechiae
Hypoplasia of arcuate nucleus
Persistence of hepatic extramedullary hematopoiesis and periadrenal brown fat
2-4 mos
SIDS
Classic Cystic fibrosis
Bronchiectasis
Pancreatic insufficiency
Male infertility
Hepatic cirrhosis
Benign tumors
Hemangiomas
Teratomas
MC tumors of infancy
Hemangioma
MC teratomas of childhood
Sacroccygeal
Malignant tumors
Neuroblastoma
Wilms tumor
MC extracranial solid tumor of childhood
Neuroblastoma
Faintly eosinophilic fibrillary material
Homer Wright paeudorosettes
Disseminated neuroblastomas with multiple cutaeneous mets
Neuropil
Blueberry muffin baby
Neuroblastoma
Homer Wright rosettes
Neuroblastoma
Medulloblastoma
PNETs
Flexner Wintersteiner rosette
Retinoblastoma
True ependymal rosette
Ependymoma
Perivascular pseudorosette
Ependymoma
Medulloblastoma, PNET, central neurocytomas, glioblastomas
MC primary renal tumor of childhood
Triphasic combination of blastemal, stromal and epithelial cell types
Wilms tumor