Paediatric dermatology Flashcards
What are the 2 categories of birthmarks in children
vascular
pigmented
What are features of a salmon patch
central / midline location facial or nuchal due to persistent foetal circulation aka angels kisses common, completely benign macular erythematous very likely to disappear
How can vascular birthmarks be divided
vascular malformation
haemangioma
what are the groups of vascular malformation
Abnormality of any vessel arterial - fast flow, dangerous, rare venous - more common, slow flow Capillary lymphatic mixture
what are haemangiomas
vascular tumours confined to childhood
rapid growth then regression
vascular malformations are more likely to regress than haemangiomas, true or false
false, haemangiomas have rapid growth but then regress in comparison to vascular malformations which do not resolve or may even progress
vascular malformations are more likely to regress than haemangiomas, true or false
false, haemangiomas have rapid growth but then regress in comparison to vascular malformations which do not resolve or may even progress
give an example of a capillary vascular malformation
port wine stain / naevus flammeus
features of port wine stain (PWS)
dark red macular lesion do not extend beyond original borders lifelong persistence usually unilateral may thicken and darken described in relation to the trigeminal nerve
what syndromes may be associated with port wine stains?
Sturge weber syndrome especially in CNV1
risk of epilepsy development
what syndromes may be associated with capillary malformation?
- Sturge weber syndrome PWS in CNV1 and ipsilateral vascular malformation in the brain –> seizures, glaucoma
- Klippel-Trenauney syndrome - capillary venous malformation and capillary-lymphatic-venous malformation, progressive limb overgrowth
PWS on lower limb
features of venous malformation/anomaly
bluish stain
if left untreated can progress severely
Mx with injection of sclerosants and coils
another name for infantile haemangiomas
strawberry naevi
what is the commonest vascular tumour in children
infantile haemangioma
benign soft tissue tumour
Can be superficial, deep to the skin or combined
epidemiology of infantile haemangiomas
90% appear within the first month of life
80% single lesion
commonest on H+N
commoner in prems and females
most undergo total/partial resolution
if they occur across the midline - concerning