Morphea Flashcards
A localized and circumscribed cutaneous sclerosis characterized by early violaceous, later ivory- colored, hardened skin. Diagnosis.
Morphea
Age. for linear and pansclerotic morphea.
Gender
20-50 in linear.
before 14 in pansclerotic
Women
Classification of various types of morphea
Circumscribed: Plaques or bands. ■ Macular: Small, con uent patches. ■ Linear scleroderma: Upper or lower extremity. ■ Frontoparietal (en coup de sabre). ■ Generalized morphea. ■ Pansclerotic: Involvement o dermis, at, fascia, muscle, and bone
Symptoms and skin findings.
SYMPTOMS Usually none .No Raynaud phenomenon. Linear and pansclerotic morphea can result in major facial or limb asymmetry,
flexion contractures, and disability. It can cause severe disfigurement.
SKINFINDINGS Plaques—circumscribed, indurated,hard,but poorly defined areas of skin; 2 to 15 cm in diameter, round or oval,
often better felt than seen.Initially,purplish
or mauve. In time, surface becomes smooth and shiny after months to years,ivory with lilac-colored edge“lilacring”
Distribution on localized and generalized.
Circumscribed:trunk, limbs, face, and genitalia; less commonly, axillae,
perineum, and areolae.
Generalized: Initially on trunk (upper, breasts, and abdomen) then thighs
What do you call a frontoparietal linear morphea.
Two linear, partially ivory-white (on the scalp) and hyperpigmented (on the fore- head)
en coup de sabre
Serologic testing is done to rule out what bacteria?
B. burgdorferi
Dermatopathology
Epidermis appears normal to atrophic with loss of reteridges.
Dermis edematous with homogeneous and eosinophilic collagen.Slight mixed infiltrate,perivascular or diffuse.
Later,dermis thickened with new
fibroblasts and dense collagen;inflammatory infiltrate at dermal–subcutis junction;dermal appendages disappear progressively
Treatment.
No effective treatment
