GI Flashcards
hirschprung disease also known as
congenital (born with) aganglionic megacolon
why are ganglionic cells important
parasympathetic nervous system uses ganglionic cells to propel stool through colon
what is hirschprung disease
a portion of colon is aganglionic (without ganglionic cells)
what happens in hirschprung disease
a portion of the bowel lacks cells needed for motility; stool just stops; continues to build up; leads to mechanical blockage/obstruction
can you see liquid stool with hirschprung disease
sometimes
s/s of hirschprung disease
chronic constipation pencil thin/ribbon-like stools fecal odor on breath lg/firm abdomen rectal sphincter fails to relax ftt vomit/diarrhea (leakage) delayed passage of meconium
high incidence of hirschprung disease in this population
down syndrome
the diseased portion of the colon looks healthy and the non diseased portion looks unhealthy, why
mechanical obstruction occurs proximal (upstream) to diseased portion making healthy part appear enlarged
what procedure may be done to help kids with enlarged colon
temporary colostomy
hirschprung disease can lead to
enterocolitis - can lead to death
where do we see hirschprung disease most
recto-sigmoid area
dx for hirschprung disease
*rectal biopsy
manmatery (how tight is internal sphincter) - balloon for rectal pressures
barium enema
most common congenital malformation of GI tract
meckel diverticulum
onset (rules of 2) of meckel diverticulum
age 2 y.o. length is usually 2 inches in length occurs 2 feet from ileo-fecal valve 2 times more common in males 2% of population suffers 2 types of tissue (stomach and pancreatic)
what condition can happen from meckel diverticulum
perforation of diverticula
can lead to enterocolitis - can die
strangulation of the bowel - can lead to blockage
vulvus/twisting of the bowel
what is meckel diverticulum
congenital disorder of developing digestive system (yolk sac)
small pouches in the wall of intestine
meckel diverticulum s/s
painless frank (bright red) bleeding
dx procedure for meckel diverticulum
nuclear medicine - meckel scan
treatment for meckel diverticulum
surgery to repair
pyloric stenosis s/s
projectile vomiting
regurgitating
irritable
palpable olive shaped mass in rt upper quadrant
visible peristaltic waves from left to right