cystic fibrosis

Question 1

cystic fibrosis affects

Answer 1

lungs (tenacious mucous)
malabsorptive disorder - mucous blocks pancreatic ducts, cant release enzymes needed to absorb (tripsin)
breathing tubes
under weight (below 5th percentile)
liver inflammation
whole body
respiratory

Question 2

steatorrhea is common in CF due to malabsorption t or f

Answer 2

true - fatty stools - under weight

Question 3

does CF affect reproduction system

Answer 3

mucous blocks vas deferns in boys makes sterile

girls think their pregnant

Question 4

kids with CF are very prone to

Answer 4

lung infections - due to mucous leads to hypoxia - chronic

Question 5

chronic hypoxia results in- a symptom of CF

Answer 5

clubbing of the fingers

barrel chest

Question 6

how do you get CF

Answer 6

inherited

exocrine disorder affecting mucous producing cells, causing thick tenacious mucous which blocks portals/ducts

Question 7

the gene for cystic fibrosis

Answer 7

CFTR gene - found on chromosome #7

cant regulate sodium and water coming out of the cells

Question 8

who is typically the first to recognize cystic fibrosis

Answer 8

parents - they claim their kid tastes salty

Question 9

cystic fibrosis and intestines - patho

Answer 9

mucous inhibits the ability to pass first stool - meconium - leading to intestinal obstruction

Question 10

cystic fibrosis and pancreatic duct

Answer 10

not producing hydrochloric acid (digestive enzymes) leading to malabsorption

Question 11

when feeding a child with CF give

Answer 11

pancreatic enzymes