Congenital heart diseases: Cyanotic HD, Acyanotic HD, Heart failure, VHD, CoA, IAA, ToF, PAVSD, PAIVS, TGA, TA, UH, TAPVC, Ebstein's Anomaly, HLHS *** Flashcards
VSD
Summarize:
Pathology
S/S
Ix findings
Management
ASD
Summarize:
Pathology
S/S
Ix findings
Management
AVSD
Summarize:
Pathology
S/S
Ix findings
Management
PDA
Summarize:
Pathology
S/S
Ix findings
Management
PS
Summarize:
Pathology
S/S
Ix findings
Management
AS
Summarize:
Pathology
S/S
Ix findings
Management
CoA
Summarize:
Pathology
S/S
Ix findings
Management
Interrupted aortic arch
Summarize:
Pathology
S/S
Ix findings
Management
TOF
Summarize:
Pathology
S/S
Ix findings
Management
PAVSD
Summarize:
Pathology
S/S
Ix findings
Management
PAIVS
Summarize:
Pathology
S/S
Ix findings
Management
TGA
Summarize:
Pathology
S/S
Ix findings
Management
Truncus arteriosus
Summarize:
Pathology
S/S
Ix findings
Management
Univentricular heart
Summarize:
Pathology
S/S
Ix findings
Management
Unobstructed TAPVD
Summarize:
Pathology
S/S
Ix findings
Management
Obstructed TAPVD
Summarize:
Pathology
S/S
Ix findings
Management
Ebstein anomaly
Summarize:
Pathology
S/S
Ix findings
Management
HLHS
Summarize:
Pathology
S/S
Ix findings
Management
Down syndrome
Dysmorphism
Cardiac defects
Turner
Dysmorphism
Cardiac defects
Williams
Dysmorphism
Cardiac defects
Noonan
Dysmorphism
Cardiac defects
Di George
Dysmorphism
Cardiac defects
Paediatric cardiac exam
General inspection features
Paediatric cardiac exam
Pulses
Pulses
Ddx Large volume strong pulse
Small volume weak pulse
Weak LL pulse
Pulsus bisfiriens
Pulsus paradoxus
Paediac cardiac exam
Precordium inspection features
Paediatric cardiac exam
Palpation features
Paediatric cardiac exam
Murmurs ddx
Risk factors of CHD
Fetal circulation and change at birth
CHD
Acyanotic and cyanotic ddx
RV & LV Pressure overload
Cause
Sign
Ix features
LV & RV Volume overload
Cause
Sign
Ix features
Pulmonary hypertension
Causes
Pulomary hypertension
Clinical, radiological, ECG Features
Eisenmenger syndrome
Mechanism
S/S
Eisenmenger syndrome
Ix
Mx
Cx
Differentiate duct dependent systemic vs pulmonary circulation vs intercircutory mixing
Pathological cause of heart failure in neonates, infants, children
Ddx cyanosis in paediatrics
Ix to differentiate causes of cyanosis in paediatrics
Ddx cyanotic CHD
Differentiate acyanotic heart disease with normal vs abnormal peripheral pulses
Ddx cyanotic CHD with/ withhout respiratory distressD
Ddx respiratory distress in neonates
Ddx failure to thrive
Ddx neonatal HF
Ddx infant HF
Ddx children/ adolescent HF
Heart failure
S/S in infants vs children/ adolescents
Paediatric HF staging
Heart failure in paediatrics
CXR features
Physiological ECG changes in neonates
Cause of chamber enlargements on ECG
Paediatric heart failure
General management framework
VSD
Size
Anatomy
Pathogenesis
VSD
S/S
VSD
Ix
VSD
Mx
PDA
Pathogenesis
PDA
Clinical features
PDA
Ix
Mx
ASD
Pathogenesis
ASD
Normal closure
Types
Result of ASD
ASD
Clinical presentation
ASD
Ix
Mx
AVSD
Pathogenesis
Types
AVSD
S/S
Ix
Mx
Valvular PS
Pathogenesis
Valvular PS
Clinical manifestations
Valvular PS
Ix
Mx
Non-valvular PS
Types
S/S
Mx
AS
Types
Pathogenesis
AS
S/S
AS
Ix
AS
Mx
CoA
Pathogenesis
CoA
Clinical presentation
Signs
CoA
Ix
CoA
Mx
Cx
IAA
Types
Pathogenesis
IAA
S/S
CoA
Ix
Mx
Mx
- Urgent PGE1/2 infusion + Inotropes + Early surgical repair
- Surgical repair: resection with end-end anastomosis, bypass graft across coarctation
- Balloon angioplasty (>4m) for discrete coarctation or re-coarctation +/- stent placement
(Cyanotic heart diseases)