Congenital Heart Disease II Flashcards
When do symptoms of ASD usually present?
not in infancy- takes a while to develop symptoms
What are the long term risks of untreated ASDs?
development of pulm vascular disease atrial arrhythmias HF
____ is the most common cyanotic heart defect and accounts for 15% of all congenital heart defects.
Tetralogy of Fallot
In Tetrology of Fallot, the RV and LV pressures are _____.
equal
Why isn’t a murmur going away a good thing?
could be a large VSD with equalizing R and L pressures elevation in PVR
When can a VSD be a right to L shunt?
with pulmonary stenosis
What are the exam findings with a small VSD?
precordial activity normal normal 2nd heart sound 2-4/6 early systolic murmur NO diastolic rumble
DX? 2-3/6 systolic ejection murmur at L upper sternal border with possible diastolic rumble widely split 2nd heart sound
ASD
Turner’s Syndrome is associated with ______.
coarctation of the aorta
Where do coarctations of the aorta occur?
in the descending aorta opposite of the ductus arteriosus or lower
DX? 1. tachycardia 2. difference in upper extremity and lower extremity BP 3. pulmonary rales 4. hepatomegaly 5. S2 and S3 gallop 6. soft systolic murmur
Coarctation of the aorta
What happens with pulmonary vascular disease at high altitudes?
it’s more common and occurs at an earlier age
10% of VSDs are which type?
muscular VSDs
What are the exam findings with a large VSD?
active precordium loud 2nd heart sound 2-3/6 harsh, holosystolic murmur loudest at the LLSB diastolic murmur
How is VSD treated?
diuretics surgical close if muscular
How does Tetrology of Fallot present?
- blue baby 2. loud murmur
What are some of the s/s of VSD?
respiratory distress diaphoresis (esp with feeding) failure to thrive tachypnea
Dx? hypoxic or hypercyanotic episode, usually in the 2-6th month of life can be life threatening unk mechanism
Tet spell (Tetralogy of Fallot)
What are the steps of atrial septal embryology?
- septum primum closes 2. apoptosis of the middle primum cells to form the osteum secundum 3. septum secundum closes to enclose the foramen ovale
What is a fixed split S2 and what is it diagnostic of?
when the S2 is split at any point in the respiration cycle; ASD
Why isn’t ASD caught at infancy?
there’s usually not a loud murmur or symptoms until later in life
What are the phys exam findings in a large ASD?
- increased respiratory rate 2. sweating with feeding 3. hepatomegaly 4. 2-3/6 systolic ejection murmur at L upper sternal border with possible diastolic rumble 5. split 2nd heart sound
What is the normal pressure within the LV?
120
How is VSD treated?
diuretics surgical close if muscular
What will happen in untreated Tetrology of Fallot?
death at the time of ductus arteriosus closure (if severe RVOT obstruction) OR cyanosis, clubbing, poor dental enamel, bleeding tendencies, squat with exercise, arrhythmias AND MAYBE cerebral abscesses
Why does a baby develop symptoms of coarctation 2 days to 2 weeks post delivery after being fine at birth?
the ductus arteriosus closes and worsens the problem
How does a secundum ASD happen?
the osteum secundum was too large or the septum secundum inadequately develops
When should you decide to surgically correct a VSD?
- pulmonary vascular changes 2. persistent symptoms, failure to thrive 3. 2a complications (aortic insuff, double chambered RV)
What is coarctation of the aorta?
a narrowing of the aortic lumen
What does the left endocardial cushion become?
posterior leaflet of the mitral valve
How does Tetralogy of Fallot happen?
abnormal development of the conal crests resulting in an infundibular septum
What will the phys exam findings be in Coarctation of the aorta?
- tachycardia 2. difference in upper extremity and lower extremity BP 3. pulmonary rales 4. hepatomegaly 5. S2 and S3 gallop 6. soft systolic murmur
Why would you want to keep the ductus arteriosus open in a Tetrology of Fallot pt?
to help offset the effects of the RV outflow tract obstruction
Why do atrial arrhythmias occur in ASD patients?
atrial enlargement over time
How does Tetralogy of Fallot happen?
abnormal development of the conal crests resulting in an infundibular septum that is displaced anteriorly, superiorly, and rightward
What are the phys exam findings in Tetrology of Fallot?
- tachycardic and cyanotic OR diaphoretic and tachypnic 2. precordial impulse at the L lower sternal border 3. 2-3/6 short systolic murmur of pulm stenosis
What causes the murmur in ASD?
- systolic ejection murmur = excessive blood flow across the pulmonic valve 2. diastolic rumble = excessive blood flow in diastole across the tricuspid valve
When should you decide to surgically correct a VSD?
- pulmonary vascular changes 2. persistent symptoms, failure to thrive 3. 2a complications (aortic insuff, double chambered RV)
How are Tet spells prevented (after the 1st one)?
beta blockers
DX? 2-3/6 systolic ejection murmur at L upper sternal border with possible diastolic rumble widely split 2nd heart sound
ASD
What are the components of S2 and what do they represent?
P2 = pulmonic valve closure A2 = atrial valve closure
What are the long term risks of untreated ASDs?
development of pulm vascular disease atrial arrhythmias HF
What is a swiss cheese septum?
multiple muscular VSDs
The murmur in a VSD is caused by?
blood flow across the defect
What is the most common congenital heart defect? How common is it?
VSD; 20% of all
What is considered a large ASD?
diameter is greater than or equal to the mitral valve size
How common are ASDs?
7-8% of all congenital heart defects
In Tetrology of Fallot, the RV and LV pressures are _____.
equal
How will a child present with coarctation of the aorta?
systemic HTN, intermittent lower extremity claudication, headaches
Why isn’t a louder murmur bad in VSD?
the VSD could be closing the PVR is low