Chapter 55 - Mucous Membrane Pemphigoid Flashcards
TABLE 55-4
Treatments for Mucous Membrane Pemphigoid
Mild Involvement
Mouth
(4)
Topical corticosteroid (gels or ointments) twice daily/4 times daily
Topical corticosteroids under occlusion (eg, dental trays)
Topical calcineurin inhibitors
Intralesional corticosteroids
TABLE 55-4
Treatments for Mucous Membrane Pemphigoid
Mild Involvement
Nose
(3)
Irrigation with isotonic saline twice daily/thrice daily
Nasal lubricants
Topical corticosteroids (eg, via sprays, inhalers)
TABLE 55-4
Treatments for Mucous Membrane Pemphigoid
Mild Involvement
Anogenital region
(2)
Topical corticosteroids
Topical calcineurin inhibitors
TABLE 55-4
Treatments for Mucous Membrane Pemphigoid
Mild Involvement
Skin
(2)
Topical corticosteroids
Topical calcineurin inhibitors
TABLE 55-4
Treatments for Mucous Membrane Pemphigoid
Moderate Involvement
Local care measures
+
Dapsone 50-200 mg daily,
Prednisone 20-60 mg each morning, OR Both of these agents simultaneously
TABLE 55-4
Treatments for Mucous Membrane Pemphigoid
Severe Involvement
Local care measures
+
- Prednisone (1 mg/kg each morning)
- Intravenous immunoglobulin (2 g/kg body weight over 2-3 days every 2-6 weeks for 4-6 months)
- Both of these agents simultaneously
+
- Azathioprine (2-2.5 mg/kg/day)
- Mycophenolate mofetil (1-2.5 g/day)
- Cyclophosphamide (1-2 mg/kg/day)
- Rituximab (375 mg/m2 weekly × 4 then every 4-6 months as needed, or 1000 mg on days 1 and 15 and then 500 mg at month 6)