CF

Question 1

what is a common insufficiency with CF?

Answer 1

pancreatic insufficiency

Question 2

what is the inheritance pattern of CF?

Answer 2

autosomal recessive

Question 3

what group of people does CF usually affect?

Answer 3

european caucasians

Question 4

what is the most common mutation in CFTR?

Answer 4

DeltaF508

Question 5

list CF complications with digestive tract

Answer 5

meconium ileus
GERD
gallstones

Question 6

list CF complications with reproductive tract

Answer 6

infertility

Question 7

list CF complications with respiratory tract

Answer 7

infections, inflammation, mucus, airflow obstruction

Question 8

list CF complications with liver

Answer 8

plugging of bile ducts, exocrine failure

Question 9

list CF complications with bone

Answer 9

osteopenia/osteoporosis

Question 10

list CF complication with pancreas

Answer 10

pancreatic insufficiency

Question 11

what is a meconium ileus?

Answer 11

obstruction of distal small intestine by meconium

Question 12

what can pancreatic insufficiency lead to in patients with CF?

Answer 12

cystic fibrosis relate diabetes

Question 13

what do you have to give CF patients with pancreatic insufficiency?

Answer 13

must give them pancreatic enzyme replacement therapy and fat soluble vitamins

Question 14

with pancreatic insufficiency, what do patients with CF not make?

Answer 14

pancreatic enzymes for food digestion

fat soluble vitamins

Question 15

how do we treat CF related diabetes?

Answer 15

give insulin…caloric restriction not advised