ATRESIA DE VÍAS BILIARES Flashcards

1
Q

QUE ES

A

COLANGIOPATÍA FIBRO-ESCLEROSANTE INFLAMATORIA QUE AFECTA CONDUCTOS BILIARES INTRA Y EXTRA HEPÁTICOS — OBLITERACIÓN Y DESTRUCCIÓN DEL TRACTO BILIAR

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
2
Q

EN QUIENES SE SOSPECHA

A

TODO RN CON ICTERICIA QUE NO MEJORA DESPÚES DE LA SEGUNDA SEMANA DE VIDA

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
3
Q

DATOS CLÍNICOS

A

ICTERICIA
COLURIA
ACOLIA

ETAPAS TARDÍAS: ANEMIA, ASCITIS Y HEPATO ESPLENOMEGALIA

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
4
Q

LABORATORIO INICIAL

A

PFH COMPLETAS: HIPERBILIRRUBINEMIA DIRECTA CON O SIN ELEVACIÓN DE ENZIMAS HEPÁTICAS

GGT > 300 EN EL 90 % DE LOS CASOS

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
5
Q

ESTUDIO DE IMAGEN DE PRIMERA LINEA

A

USG ABDOMINAL

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
6
Q

TRATAMIENTO

A

QUIRÚRGICO CON CIRUGÍA DE KASAI
SIN EL MORTALIDAD DE 100%

ANTES DE LOS 60 DÍAS DE VIDA

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
7
Q

ESTUDIO DE IMAGEN MAS SENSIBLE

A

GAMMAGRAFIA HEPATOBILIAR

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
8
Q

MALFORMACIONES CONCOMITANTES MAS COMUNES

A

CARDIACAS

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
9
Q

COMPLICACION PRINCIPAL

A

CIRROSIS HEPATICA TEMPRANA

How well did you know this?
1
Not at all
2
3
4
5
Perfectly