24.1 Paeds Rheumatic Diseases

Question 1

Dangers of Kawasaki disease in developed world?

Answer 1

Number one cause of acquired heart disease: coronary artery dilatation/aneurysms

Question 2

80% of Kawasaki disease happens when?

Answer 2

<5years, males

Question 3

Kawasaki remains a?

Answer 3

Clinical diagnosis

Question 4

Important things to ask parents re Kawasaki?

Answer 4

Fevers for 5-10 days

• red hands or feet/peeling? Distally to proximal
• Conjunctivitis
• swollen neck nodes
• rash?

Question 5

5 main features of Kawasaki?

Answer 5

5 days of fever
Rash
Conjunctivitis
Mucositis
Peripheral changes
Cervial lymphadenopathy

Question 6

Treatment of kawasaki?

Answer 6

Referral/admission
IVIG 2g/kg
Aspirin 5mg/kg
ECHO in acute phase

Question 7

Follow up for kawasaki?

Answer 7

• 12 month ECHO

- delay live immunisations for 9 months

Question 8

Henoch-Schonlein pupura typical features

Answer 8

Small vessel vasculitis
-rash non-blanching
Tendons around ankles
Joint swelling
Abdo pain
Scrotal swelling

Question 9

Henoch-Schonlein pupura affects where in joint?

Answer 9

Serosa

Also why you get Abdo pain etc.

Question 10

Systemic Lupus Erythematosus more common which populations?

Answer 10

Blacks, hispanics, asians

Question 11

Who usually gets Systemic Lupus Erythematosus?

Answer 11

<18 year old average 11-14

5:1 females

Question 12

Systemic Lupus Erythematosus what kind of ulcer?

Answer 12

Oral palatal ulcer: not painful, almost pathopneumonic

Question 13

Juvenile dermatomyositis features?

Answer 13

• Periocular rash
• Gottron’s Papuans on hands, can look like eczema
• trouble keeping up with peers

Question 14

What is plaque morphea?

Answer 14

Limited scleroderma, mostly cutaneous