20-2 (congenital) Flashcards
What does congenital renal disease most often result from?
Acquired developmental defect during gestation
Congenital renal anomalies should prompt what?
Evaluation of other organs
– simultaneous development
Prune Belly Syndrome usually occurs in?
Males
What are 4 possible characteristics of Prune Belly Syndrome?
- Bilateral Hydroureteronephrosis
- Vesicoureteral Reflux
- Renal Dysplasia
- Bilateral Cryptorchidism
What are 4 possible characteristics of Prune Belly Syndrome?
- Bilateral Hydroureteronephrosis
- Vesicoureteral Reflux
- Renal Dysplasia
- Bilateral Cryptorchidism
What is Hydroureteronephrosis and with what disease is it almost always present?
Kidney and ureter swell due to obstruction of urine flow
– Prune Belly Syndrome
What is the Vesicoureteral Reflux?
Urine flows in the opposite direction of normal
What is Cryptorchidism?
Testes are intra-abdominally at the level of the iliac arteries
Babies with Prune Belly Syndrome will likely develop what 2 infections and/or need a renal transplant?
UTI
Pyelonephritis
What is a hereditary malignant tumor of the kidneys?
Wilms tumor
When is Bilateral Agenesis of the kidneys seen?
Incompatibile with life – stillborns
Unilateral Agenesis of a kidney is compatible with life if no other issues are present. How will that one kidney that is present likely look and what may develop in it?
It will be enlarged due to adaptation
– glomerular sclerosis may form
If bilateral renal hypoplasia is present, what will present in early childhood?
Renal failure
What are the 3 characteristics of true renal hypoplasia?
- Seen in low birth weight infants
- NO scars
- < 6 lobes/pyramids
What are the 3 characteristics of true renal hypoplasia?
- Seen in low birth weight infants
- NO scars
- < 6 pyramids/lobes