UWORLD - PEDIATRICS (Mixed)

Question 1

Most common predisposing factor to bacterial sinusitis?

Answer 1

VIral URI

Question 2

Pt with varus of calcanus and talus and adduction of the foot - suspected diagnosis? Management?

Answer 2

Clubfoot

Serial casting immediately

Question 3

Pt presents with thrombocytopenia, rash, and multiple infections - suspected diagnosis?

Answer 3

Wiskott-Aldrich

WIPE
Wiskott-Aldrich
Infections
Purpura (thrombocytopenia)
Ezcema

Question 4

Von Geirkes vs Debranching emzyme deficiency?

Answer 4

Normal LFTs but elevated lactate and uric acid

Elevated LFTs, but normal lactate and uric acid

Question 5

Floppy baby with macroglossia and heart failure - suspected diagnosis? deficiency in?

Answer 5

Pompe’s disease

Acid maltase

Question 6

Cause of infant respiratory distress syndrome? Risk factors?

Answer 6

Surfactant deficiency

#Prematurity
#Maternal disbetes mellitus

Question 7

Pt with light brown skin spots, and precocious puberty?

Answer 7

McCune-Albright

Question 8

Birth defect of nail/digit hypoplasia - causal drug?

Answer 8

Phenytoin

Question 9

Birth defect of thin upper lip - causal drug?

Answer 9

alcohol

Question 10

Acidified glycerl lysis test used to diagnose?

Answer 10

Spherocytosis

Question 11

CD55 and CD56 protein testing on RBCs used to diagnose?

Answer 11

Paroxysmal nocturnal hemoglobinuria

Question 12

Only immunocompromised pts get this immunoglobulin upon exposure?

Answer 12

VZV

Question 13

Treatment for tricyclic intoxication? (Why?)

Answer 13

Sodium Bicarb

Corrects acidosis and narrows QRS prolongation

Question 14

Neonate presents with bilious vomiting and bloodstained stools - suspected diagnosis? best initial test? Most accurate?

Answer 14

midgut volvulus

Xray (to r/o pneumoperitoneum)

Upper GI series

Question 15

Neonate presents with non-bilious vomiting - suspected diagnosis?

Bilious vomiting?

Answer 15

pyloric stenosis

volvulus (intussception not found as neonate)

Question 16

Most common predisposing factor for orbital cellulitis?

Answer 16

bacterial sinusitis

Question 17

Child presents joint pain soon after viral illness - suspected diagnosis? Management?

Answer 17

Transient synovitis

Ibuprofen and rest (NOT joint tap)

Question 18

Primary deficiency if:

1. Absent B-cells and low Immunoglobulins?
2. Normal B-cells and decreased immunoglobulins
3. Normal B-cells but low IgA
4. Normal B-cells, low immunoglobulins expect for IgM?
5. Normal B-cells and decreased IgG

Answer 18

1. Agammaglobulinemia
2. Common Variable immunodeficiency
3. IgA deficiency
4. Hyper-IgM
5. IgG Subclass deficiency

Question 19

Triad of congential toxoplasmosis?

Answer 19

#chorioretinitis
#hydrocephalus
#intracranial cacifications

Question 20

Congenital Rubella triad?

Answer 20

Deafness, cateracts, and cardiac cardiac defects

Question 21

hepatospenomegaly, skin ulcerations, rhunorrhea

Answer 21

Congenital syphilis

Question 22

Sand-paper like rash - suspected diagnosis? Other ORAL findings?

Answer 22

Scarlet fever

#Strawberry tongue
#Gray exudates

Question 23

Hyperventilation can induce what type of seizure?

Sleep deprivation?

Answer 23

Absence

Juvenile myoclonic

Question 24

Treatment for RSV?

Answer 24

Palivizumab IF
#Preterm birth
#Lung disease of prematurity
#congenital heart disease

Question 25

Treatment for Bullous vs non-bullous imetigo?

Answer 25

Oral Abx (cephalexin, dicloxacillin) vs topical (mupirocin)

Question 26

Unilateral cervial adenitis - in otherwise healthy child treatment?

if preschool-aged, nontender, and slower onset?

Answer 26

Clindamycin (Staph, strep)

Macrolide (mycobacteria)

Question 27

Mechanism of arthopathy in hemophilics?

Answer 27

iron/hemosidern deposition leading to synovitis and fibrosis

Question 28

Microvesicular fatty liver vs macrovesicular fatty liver?

Answer 28

Reye syndrome (children) vs obesity/EtOH (adults)

Question 29

Refeeding syndrome - surge in what hormone? Why deadly?

Answer 29

Insulin

Promotes uptake of phosphorus, K, and Mg (as serum levels drop, pt can develop arrhythmias)

Question 30

Pt with epistaxis, visable mass and bony erosion - suspected diagnosis?

Answer 30

Juvenile Angiofibroma