THORACIC Section 13: Systemic Flashcards
Collagen Vascular Disease Pulmonary Manifestations
More pleural effusions and pericardial effusions than with other connective tissue disease
Lupus
Collagen Vascular Disease Pulmonary Manifestations
Fibrosis is uncommon. Can get a “shrinking lung.”
Lupus
Collagen Vascular Disease Pulmonary Manifestations
Looks like UIP and COP. Lower lobes are favored.
Rheumatoid Arthritis
Collagen Vascular Disease Pulmonary Manifestations
Reticulations with or without honeycombing, and consolidative opacities which are organizing pneumonia
Rheumatoid Arthritis
Collagen Vascular Disease Pulmonary Manifestations
NSIP > UIP; lower lobe predominant findings.
Scleroderm
Collagen Vascular Disease Pulmonary Manifestation
Dilated fluid filled esophagus.
Scleroderma
Collagen Vascular Disease Pulmonary Manifestation
Lymphoid interstitial pneumonia
Sjogrens
Collagen Vascular Disease Pulmonary Manifestation
Extensive ground glass attenuation with scattered thin walled cysts.
Sjogrens
Collagen Vascular Disease Pulmonary Manifestation
Upper lobe fibrobullous disease
Ankylosing Spondylitis
Collagen Vascular Disease Pulmonary Manifestation
Usually unilateral first, then progresses to bilateral.
Ankylosing Spondylitis
Rheumatoid Arthritis + Upper Lobe Predominant Lung Nodules.
Caplan Syndrome
The nodules in this syndrome can cavitate and may have pleural effusion
Caplan Syndrome
This is a progressive loss of lung volume in both lungs seen in patients with Lupus
“Shrinking Lung”
“S”hrinking “L”ung of “SLe”
Most common manifestation of SLE in Chest
Pleurifis with/without pleural effusion.
This is seen in liver patients with the classic history of “‘shortness o f breath when sitting up.’”
Hepatopulmonary syndrome
Opposite of CHF
What Happens in Hepatopulmonaryu Syndrome?
Distal vascular dilatation in the lung bases (Subpleural telangiectasia) + dilated subpleural vessel (Doesnt taper)
What is the classic tirad of Wegener Granulomatosis (Granulomatosis with Polyangitis)
Upper tract, lung, and kidneys (rare)
Lung 95%
Most common presentation of Wegener Granulomatosis
Nodules with cavitation in random distribution (half of them cavitating)
GG changes with hemorrage
Diagnosis?
Wegener Granulomatosis
Autoimmune Pulmonary renal syndrome favoring young men
Goodpasture Syndrome
Bilateral coalescent opaciteis that look like edema (but are hemorrhage)
Goodpasture Syndrome
What can occure from recurring episodes of bleeding in Goodpasture Syndrome?
Pulmonary hemosiderosis wiht iron deposition seen as small, ill-defined nodules