Systemic Diseases Flashcards
Takayasu
Women of childbearing age Large vessel vasculitis Stenosis of aneurysms of aorta / branches Subclavian stenosis HTN, TIA/CVA, myocarditis, vasculitis
Relapsing polychondritis
Aortic or mitral valve disease, AR
Hemochromatosis
Normall wall thickness
DCM, hepatic dz, DM, tanned skin
Arrhythmias, conduction abnormalities
Restrictive filling
Eosinophilic heart disease
Apical thrombi, endocardial thickening
Restrictive
Leaflet entrapment, MV > TV, MR and TR
Biatrial enlargement
Carcinoid
GI tumors
Usually right sided valves, thickening and reduced mobility
Drug-induced valvular disease
ErgotsLooks like rheumatic
Vitamin deficiency associated with cardiomyopathy
Selenium
Thiamine
Carnitine
Thiamine deficiency
High output heart failure
Selenium deficiency
TPN
Cardiac enlargement and systolic heart failure
Carnitidine deficiency
TPN or genetic defect
Systolic dysfunction
Chagas echo
BIventricular enlargement
Ventricular wall thinning
Apical aneurysm
Mural thrombi
Friderich ataxia
Autosomall recessive
Concentric hypertrophy mimicking HCM
Globally decreased EF, LV-end diastolic diameter
GPA echo
Small vessel vasculitis
Regional WMA not in typical coronary distribution
Amyloid echo
LV wall thickening
DD
Progression to restrictive CMY with non dilated or small cavity
Sarcoid echo
LV systolic dysfunction RWMA in non-coronary distribution Abnormal wall thickness Perfusion defects in anteroseptal and apical regions AV block
Risk factors for peripartum CMY
Age > 30 Multiparity African descent Pregnancy with multiple fetuses Preeclampsia / eclampsia Postpartum hypertension Oral tocolytics
Cardiac manifestations of HIV
Pericardial effusion (most common) DCM Primary pulmonary hypertension Kaposi sarcoma CAD
Pheochromocytoma
HTN
Reversible WMAs
DCM
Cushing syndrome
Excess glucocorticoid
Moderate chronic diastolic HTN
Rheumatoid arthritis
CAD, diastolic dysfunction
Takotsubo
Transient apical and mid ventricular WMAs
Dynamic LVOT obstruction, RV apical dysfunction may occur
Scleroderma
Pericardial effusion
Systemic and pulmonary hypertension
May have systolic / diastolic dysfunction
Libman Sacks endocarditis
SLE
Small verrucous valvular lesions, usually MV, ventricular aspect
Fabry disease
Angiokeratomas, neuropathic pain, teleangiectasias, heat intolerance, GI symptoms, renal manifestations Concentric LV hypertrophy Myocardial dysfunction Aortic and mitral valve abn Conduction abnormality
Tuberous sclerosis
Neurocutnaeous disorder, hamartomas
Rhabdomyoma - kids, benign, multiple, ventricular walls or AV valves
Marfan syndrome
Pear shaped dilatation of aortic root
Extra-adrenal paraganglioma
Headache, sweating, tachycardia
Like pheochromocytoma
Carney syndrome
Autosomal dominant
Myxoma, schwannoma, endocrine tumors
Pigmentation abnormalities
