Physical activity recommendations for children with specific chronic health conditions: Juvenile idiopathic arthritis, hemophilia, asthma and cystic fibrosis Flashcards
What is the prevalence of JIA?
1 in 1000 children
How many subtypes of JIA are there?
Seven
What is the definition of chronic arthritis?
Presence of joint swelling or by two or more of the following: 1. Joint pain 2. Warmth 3. Limited ROM For at least 6wks
What constitutional signs or symptoms are associated with JIA?
- Anorexia
- Weight Loss
- Growth failure
- Fatigue
What extra-articular manifestations are associated with JIA?
- Ocular
- Cardiac
- Pulmonary
- Hematopoietic involvement
What percentage of JIA persists to adulthood?
55%
What are the potential benefits of exercise in JIA?
- Improves aerobic fitness
- Better muscle strength and function
- Decreases disease activity
- Improves self-efficacy
- Improves energy level
- Improves quality of life
- Reduces pain and medication use
- Optimize bone mineral density
- Reduced obesity
What are the potential risks of exercise in JIA?
- If cervical spine arthritis increased risk of spinal cord injury
- If TMJ disease increased risk of dental injury
- Possible risk of cardiovascular complications with exercise
- If uveitis at increased risk of eye injury
What are the recommendations for exercise in JIA?
- Can safely participate in sports without disease exacerbation.
- Should participate in moderate fitness, flexibility and strengthening exercises.
- Can participate in impact activities and competitive contact sports if their disease is well controlled and they have adequate physical capacity.
- Should be encouraged to be physically active as tolerated. Those with moderate to severe impairment or actively inflamed joints should limit activities within pain limits.
- Should gradually return to full activity following a disease flare.
- Should take individualized training [especially for children with severe joint disease) within a group exercise format for physical/social benefit.
- Physiotherapists on paediatric rheumatology health care teams should coordinate individual exercise programs.
- Should have radiographic screening for C1-C2 instability before participation in collision/contact sports if they have neck arthritis. If present, further evaluation is required.
- Should wear appropriately fitted mouth guards during activities with jaw and dental injury risk (per general population), especially if they have jaw involvement.
- Should wear appropriate eye protection (per general population) during activities with ocular injury risk
What is the inheritance of hemophilia?
X linked recessive
What is the incidence of hemophilia?
1 in 5000
What are some clinical features of hemophilia?
- Joint or muscle hemorrhage
- Easy bruising
- Synovitis and joint degeneration and arthritis
What are potential benefits of exercise in hemophilia?
- Fewer bleeding episodes
- Increased joint stability
- Increased periarticular muscle strength
- Improve bone mineral density
- Aerobic exercise may have beneficial effect on coagulation
What are potential risks of exercise?
- Risk of life threatening bleeding episode
2. Hemophilic arthropathy
What are the recommendations regarding exercise in children with hemophilia?
- Should receive appropriate factor prophylaxis to reduce the risk of bleeding in sport.
- Should undergo vigilant assessment of joint and muscle function before sport selection. If restrictions are required, physicians should counsel children and their families about safe alternatives.
- Should be carefully assessed before allowing participation in contact or collision sports such as martial arts, hockey or football. Consultation with a sport medicine physician and/or paediatric hematologist may help.
- Require written strategies (coach, parent or school) before sport participation to prevent or treat bleeds.
- Should wear protective equipment, undergo physical therapy or take prophylactic factor replacement therapy.
- Require factor replacement, ice, splinting and rest to manage acute bleeds. Physical activity should be avoided until joint pain or swelling has resolved. Return to sport requires individualized assessment and appropriate rehabilitation.