Peds 3 Flashcards
cyanotic newborn that doesnt improve with O2
ToGV
newborn holosystolic murmur that worsens with inspiration
ebstein’s anomaly
Arrhythmia a/w ebstein’s anomaly
WPW syndrome
Newborn cyanotic with holosystolic murmur that requires a VSD or* ASD to survive, EKG w/ LVH
Tricuspid Atresia
CHD with increased pulmonary blood flow and biventricular hypertrophy
truncus arterosis
Harsh holosystolic murmur over left lower sternal border. Loud P2
VSD
fixed and split S2. systolic ejection murmur with diastolic rumble
Endocardial cushion defect
newborn with bounding pulses and widened pulse pressure
PDA
PDA a/w (2)
prematurity and congenital rubella
rosary bead appearance of ribs
Vit D deficiency
kid with murmur that increases with valsalva, standing and exercise
HCM
joint and chest pain, rash, elevated ESR, prolonged PR interval
acute rheumatic fever
Tx acute rheumatic fever
erythromycin 10d then prophylaxis until age 20
Tx meconium ileus
gastrografin enema BEFORE considering surgery
Tx pneumonia in CF
ceftazidime, piperacillin or tobramycin
asthma: daily and nightly cough, FEV1 less than 60. dx and tx
Severe persistent = albuterol, inhaled corticosteroid, long-acting BA (salmeterol), monteleukast +/- oral steroids
asthma 2x/wk no night sx, dx/tx
mild intermittent, tx = albuterol
asthma 4x/wk + nightly cough 2x/mo, normal PFTs, dx/tx
albuterol and inhaled corticosteroids
asthma daily + nightly cough 2x/wk and FEV 60-80, dx/tx
moderate persistent, tx = albuterol, inhaled CS and salumeterol (long acting BA)
common infxn in asthmatics
allergic bronchopulmonary aspergillus
hematuria only 1-2 DAYS after a runny nose/sore throat, dx?
Berger’s Disease = IgA nephropathy
smoky or cola- urine
PSGN
subepithelial IgG humps
PSGN
Dx PSGN
ASO titer
hematuria and hemoptysis
Goodpasture’s
hematuria and deafness
Alport’s, X-linked recessive
Tx calcium oxalate stones
hydrochlorothiazide
kid with FHx of renal stones, MC type?
cystein
kid with indwelling catheter and alkaline urine, MCCs?
struvite stone = proteus, staph, pseudomonas or klebsiella
Tx MCD
prednisone 4-6wks
immunizations especially important in MCD
varicella and pneumococcus b/c they leak Ig’s into their urine
kid with proteinuria suddenly develops flank pain, Dx?
renal vein thrombosis 2/2 peeing out ATIII, protein C/S –> stat renal US or CT
sicke cell patient with respiratory distress that requires emergency tonsillectomy?
Waldyer Ring’s hyperplasia
MCC death in sickle cell
acute chest syndrome 2/2 pulmonary infarct
tx stroke in sickle cell
exchange transfusion! do NOT give tPA
prophylaxis in sickle cell
Penicillin from 2mo-6yrs?
Tx thalassemia
transfusion +/- deferoxamine
Deficiencies in goat’s milk
folate and vit B12
3 month old. Normal platelet. Normal WBC. Anemia. Increased RBC ADA and low reticulocytes. Triphalangeal thumb. Dx? Tx?
Blackfan Diamond Anemia
Tx = steroids, transfusions +/- stem cell transplant
Pathophys Fanconi’s anemia, complications?
2/2 chromosomal breaks, complicationcs inculde increased risk AML and other cancers
2yo with hyperactivity, developmental delay, abd pain and constipation
lead poisoning
succimer if >46, EDTA if>70
epistaxis, heavy menses, petechiae. Normal platelets. Increased bleeding time and PTT. DX? Tx?
vWD
Tx = DDAVP + factor 8 replacement
epistaxis, heavy menses, petechiae and DECREASED platelets, dx/tx
ITP
tx = IVIG, prednisone +/- splenectomy but do NOT give platelets (simply worsens consumptive coagulopathy)
1st clotting factor to deplete
factor 7
cloting factors NOT affected in Wilson’s disease
8 and vWF because they are made in ENDOTHELIAL cells
causes of HUS (4)
E. coli, shigella, salmonella, campylobacter
IgA and C3 deposition in skin
Henoch-Schlonen Purpura
Kid with lower extremity rash, abd pain and joint pain
Henoch-Schonlein Purpura
MC brain tumor in kids
pilocytic astrocytoma of cerebellum
2nd MC brain tumor in kids, what is the worst prognostic factor?
Medulloblastoma, worst prognosis if in vermis
kid with abd mass that doesn’t cross midline and HTN
Wilm’s Tumor
Wilm’s tumor a/w?
WAGR = Wilms, aniridia, GU abnormalities, Retardation
Hemihypertrophy
Beckwith-Weidmann syndrome