PEDI 14 Flashcards
Cystinuria pathophysiology?
Inability to transport diphasic amino acid-like cysteine, ornithine.lysine, and arginine in renal tubular cell and intestine.
CM?
Recurrent Cysteine stone(unlike other AA not water soluble)
Hexagonal,radiolucent stone
Cyanide NP test help to diagnose by detecting cysteine levels in urine
Family Hx of nephrolithiasis
GI complication of HSP?
Intussusception(MC)–Iliocolic is common
GI bleeding
Perforation
Treatment of neonatal Clavicular #?
Reasurance Gentele handling Analgesics Place the affected limb on a long sling and 90-degree flexion Heal by itself within 7-10 day
lumbar vertebral spondylolisthesis CM?
Common in age 10-19(groeth spurt and phy. lordosis)
Athletes with repetitive lumbar flexion and rotation
Palpable steep off on lumbar area(vertebral bodies seepage)
Bilateral or unilateral radioculophaty
Due to # of pars interreticularis)
x-ray feature of the cause of neonatal RD?
TTN: Bilateral Perihilar linear streaking
NRDS: Defuse ground-glass opacity, AB, low lung volume
PPHtn: Clear lung with a decrease vascularity
NRD risk?
Prematurity (almost all neonates <28 weeks)
BW <1500
Due to immature lung inability to produce surfactant
Management?
continuous PAPV
surfactant replacement and MV reserved for sever case
MAS X-Ray?
Term or post-term MSAF Bilateral patchy infiltration Coarse streaking on both lung fields Flattening of diaphram
Lisch nodule?
raised,tan-colored hamartoma of iris
NFT1
Brushfield spot?
Whitish gray spot in the periphery of IRIS
DS
Cause of acute bacterial rhinosinusitis?
Non-typable H.influenza-45%
S,pnumonia–25%
M.Catheralis–25 %
management?
Amoxacline and clavulanate
Are sinuses present at birth?
ethmoid and maxillary
Symptom of focal seizure?
Motor(Twitching…)
sensory(Parastesia…)
Autonomic(Sweating…)
May have semi purposeful automatism(chewing, picking)
May have LOC/Tods paralysis following the seizure
Management?
EEG(during seizure there will be abnormality) Brain MRI(more associated with ICSOL than GS)
What signs make you suspect urethral injury?
Blood at meatus
Haematuria (pink urine)
Urinary retention
what to do?
Retrograde cystourethrography(see contrast extravasation) immediately before any procedure?
Duodenal atresia CM?
MC GI complication of DS
Bilious vomiting in first 2 day
Failure to pass meconium
On x-Ray(double bubble sign and Absent bowel gas)
Management?
D/C oral feeding
NG tube decompression
Immediate surgical repair