Ped1 Flashcards
which vitamin is deficient in milk?
VitD and Vit A
X-ray in ricket?
Winding of metaphysis
Ricket treatment?
Vit D and Ca
Cause of Niemann-pick disease?
sphingomyelinase deficiency
AR
CM?
loss of motor milestone 2-6 month
Chery red macula
Hepatosplenomegaly
Hyporeflexia/areflexia
How to d/t from tay-sacks disease?
in Tay saks
b-hexosaminidase deficiency
No hepatosplenomegaly
Hyperreflexia
Biliary duct cyst?
cystic dilation of bile duct
single and extrahepatic form common
CM?
majority of patients <10 RUQ pain RUQ palpable mass Obstructive Jaundice with acholic stool Elevated Panc.Enzyme due to pancreatitis in old children or reflex of pan. enzyme
Diagnosis and Managment?
Diagnose with abdominal U/S Managment Tumor resection(relieve obstruction and reduce risk of cholangiocarcinoma transformation)
How to d/t from biliary atresia?
In biliary atresia, there will be Hepatomegaly Absent visible gallbladder Present with infancy (2-8) week No pancreatic enzyme elevation In U/S absent gall bladder/BD/CBD Intraoperative cholangiography is GS for diagnosis
Managment of BA?
Surgical hepato-portoenterpstomy (Kasai procedure)
Liver transplant
Breast milk jaundice?
A peak in the second week
Due to B-glucoronidase in milk-deconjugate intestinal bilirubin
Unconjugated hyperbilirubinemia
Neuroblastoma pathogenesis?
Neural crest origin
Involve adrenal medulla and sympathetic chain
CM?
Midian age < 2 Abdominal Mass Fever, weight loss Opsoclonus(rapid eye movt-Myoclonus(rapid extremity jerking movt) syndrome Periorbital echemosis Spinal metastasis
Diagnostic evaluation?
Increase catecholamine metabolite
Small, round blue cell tumor
N-myc gene amplification
Indications for non-contrast CT in pediatric TBI?
LOC
AMS
Foccal nurogic sighn
sever mechanism of head injury((fall(in-age <2,>0.9m in >2(fall >1.5m//MVC?high impact)
Non frontal scalp hematoma and palpable skul # in <2
Vomiting,S.Headache,basilar Skul # in age 2-18
Steeps of neonatal resuscitation?
Dry and stimulate
Clear suction
Provide warmth(skin to skin)
when to do first?
Term
Breath/cry
Appropriate tone
If above the APGAR will be 9
Ahy tracheal suctioning is not recommended?
Stimulate vagus–apnea/bradychardia
Indication for the cardiac monitor?
Bradycardia(<100)
Apnea
Gasping
The patient requires chest compression