Pead 5

Question 1

Neonatal herpes symptoms pathogenesis?

Answer 1

Intrautine(rare but fatal)
Intrapartum(coomon in active viganal infection)
postpartum(if there active sore)

Question 2

CM?

Answer 2

Mucocutaneous vesicle and keratoconjunctivitis
CNS form:Seizure, fever, and lethargy
Dissiminated:Sepsis, hepatitis, and pneumonia

Question 3

Imaging?

Answer 3

Temporal heamorage and edema

Question 4

Managment?

Answer 4

Acyclovir

Question 5

Transient synovitis pathogenesis?

Answer 5

Inflamation of tissue surounding Hip joint

Question 6

CM?

Answer 6

3-8 year
No fever
joint pain
Limping
Decrease hip joint movt
Keep hip in flexed and external rotation in supine(wide joit space)
Resist I.rotation and extension
Resolves whithin 1-4 week
Able to bear wight

Question 7

Diagnosis?

Answer 7

Near normal CBC.eSR and CRP

U/S of hip:Unilateral/bilateral hip effiution

Question 8

Managment?

Answer 8

Suportive

NSAID

Question 9

Primary humoral deficiency CXS?

Answer 9

Recurent and sever sinopulmonary infection by virus and encapsulated organ.

Question 10

What are the causes?

Answer 10

BA
H IgM S.
CVID
Ig A deficiency
Selective Ig g deficiency

Question 11

How to D/T?

Answer 11

BA–Low B-cell

Other–Normal B cell

Question 12

What to do next?

Answer 12

Classify based on Ig level

Question 13

When will be Thyroglosal Cyst diagnosed?

Answer 13

When infected after RTI

Question 14

Having immaginary friend is normal in which age?

Answer 14

3-6

Question 15

Effect on child?

Answer 15

Benificial(improve creativity and rehersal for good social intraction)

Question 16

Other normal bizzare behaviour in thise age?

Answer 16

Dressed -UP
Pretend play
Story telling with fanciful details

Question 17

Facial menifestation of anaphlaxis?

Answer 17

Conjectival redness and B.pain and periorbital edema

Tongu and lip swelling

Question 18

Alport syndrome genetics?

Answer 18

X-linked recesive

Due to type IV collagen defect

Question 19

CM?

Answer 19

Renal:Asymptomatic Heamaturia and Progresive RI
 ----+/- rotinuria and HTN
SN hearing loss
Anterior lenticonus(lence protrusion)
Groos heamaturia after RTI

Question 20

Diagnosis?

Answer 20

Molocular
Longtiudnal GBM spliting
Norml complement

Question 21

Neonatal sepsis sign?

Answer 21

Sepsis sign
lethargy
Poor feeding
Jaundice(sepsis imair conj.)

Question 22

Investigasion?

Answer 22

CBC
LP
Blood culture
Urinalysis

Question 23

Why we do LP w/o head CT in neonate?

Answer 23

Because of open fontanel they have no herination risk

Question 24

What sighn help to D/T Hemocystinuria from MS?

Answer 24

Hemocystinuria is 
Autosomal recessive
Due to cystionin syntase deficiency
Intelectual disablity
Thrombosis risk
Downward lence orientation
Fair cmplexion(blu sclera and skine)
Megaloblatic anemia

Question 25

Managment?

Answer 25

``` B-6 Folic acide B-12 Cystionin Antiplatelet/Anticoagulant ```

Question 26

what about ehler dhalol?

Answer 26

No disproporsionate bodie | No lense dislocation

Question 27

Aplastic anemia pathophysiology?

Answer 27

MCC aplastic anemia Bone marow failure Due to DNA repair deffect

Question 28

CM?

Answer 28

``` Sort stature Hypoplastic tumb/thenar athrophy Polyductyly Hyper/Hypoppigmentation Genitourinary malformation ```

Question 29

LAB?

Answer 29

``` Pancytopnia Megaloblastic anemia(erythropoisis) posetive chromosoal breakage ```

Question 30

Managment

Answer 30

Steem cell translantation

Question 31

Fungal ottitis externa Cxs?

Answer 31

Occur after bacterial OE Insidious onset Aspargilus and candidia White friable derbis

Question 32

Croup pathophysiology?

Answer 32

Due to Parainfluena infection of larhnex and thrachia Larengio-bronchitis Subglotic sweeling(x-ray)

Question 33

CM?

Answer 33

Inspiratory stridor Hoarsenesness Barking cogh

Question 34

Managment?

Answer 34

o2 if Spo2 <92 Mild(no stridor at rest): Cs + humid air Sever(stridor at rest):Cs + nabulizer ephiniphrine MV if have sighn or RF

Question 35

Sever combine ID sighn?

Answer 35

Recurent/Sever viral/bcterial ,oportunstic and fungal infection Chronic diarrhea Growth restriction

Question 36

Pathophysiology?

Answer 36

``` Absent CD3(T cell)(developmental defect) B-cell dysfunction due to absent T cel ```

Question 37

Managment?

Answer 37

T-Cell steem cell transplantation

Question 38

Drug should be avoided in G6PDH deficiency?

Answer 38

``` Dapsone Isobutyl nitrate Nitrofurantoin Primaquine Rasburicase ```

Question 39

Cause of congenital lymphedema?

Answer 39

Lymphatic chaneel defect due to lymphatic NTW dysgenesis.

Question 40

Vit A importance in Measel?

Answer 40

Decrease morbidity and mortality | By improving Ab formation and reepithelization

Question 41

Measel complication?

Answer 41

encephalitis Pnumonia Blindness

Question 42

In who to give?

Answer 42

``` extreme age(old and children) Imunocompromized Vit A deficeint Pregnant Require hositalization ```

Question 43

CM?

Answer 43

Predorm(cogh,coryza,koplic spot,fever,conj.) | Rash(cephalocaudal,centrifugal)

Question 44

How pertusis cause facial petiche and subconjectival heamorage?

Answer 44

Because of high intrathoracic P--capillary injury

Question 45

mamography is not good at?

Answer 45

If age <30--large breast tishu make difficult for assesment

Question 46

Fibroadinoma cxs?

Answer 46

Common in upper outer quadrant | Perimenestrawal mass tenderness

Question 47

generaly breast ca rare in adolecent and chikdren?

Answer 47

Yes

Question 48

cause NRDS?

Answer 48

Prematurity DM c/S Perinatal asphexia

Question 49

Diagnosis of cartenger?

Answer 49

intranasal NO

Question 50

Common cause of atroke in children?

Answer 50

``` SCD Protrombic disorder CHD Bacterial meningitis Vasculitis Foccal cerebra; artheriohaty Head/Neck trauma ```