Paeds 8 Flashcards
What conditions are associated with undescended testes?
Prader- Willi Syndrome
Kallmann
What are the complications of PUV?
Renal failure
Dysfunctional bladder
Infertility
What are the causes of VUR and how are they investigated?
VUR refers to a defect which results in urine flowing back up the ureters and into the kidney.
Primary:
This is a defect at the trigone region where the anti-reflux mechanisms fail.
- abnormally situated ureteric orifice
- Larger than normal orifice
Secondary:
This is when there is not a specific issue with the trigone region but instead a defect elsewhere
- Posterior urethral valves
- Dysfunctional bladder
Investigations:
- MCUG
- DMSA scan
Management:
- correct defect.
- prophylactic antibiotics
- anti-cholingerics
Surgical for primary:
- STING procedure (bulks the opening of the ureter)
- Valve ablation if PUV
What are you’re main differentials in ITP?
Henoch-Scholien Purpura
Leukaemia
Meningitis
HUS
DIC
What the prognosis of minimal change disease?
1/3rd fully recover
1/3rd relapse
1/3rd continually relapse
How is rheumatic fever treated?
Aspirin
One off dose of IM benzylpenicillin
followed by:
Penicillin V
Steroids can be used for Sydenham’s chorea
Best rest for joint pain
What is the prognosis of Henoch Scholien Purpura?
1/3rd relapse
<5% have severe renal failure
What is management of ITP?
Watch and wait. Avoid NSAIDs and Aspirin
- increases bleeding
If severe:
- Immunoglobulins and steroids
Major bleeding:
- FFP and splenectomy
What is the investigations one should do into Henoch scholien to rule out more sinister cause?
FBC
- infection
Blood film
- blast cells
Coagulation
- bleeding disorder
- infection
How many children have a re-occurrence of Hencoh Scholien
30%
What is the steroid regime for minimal change disease? And what are other aspects of the management?
High dose for 8 weeks on a reducing regime
- Albumin infusion
- Prophylactic antibiotics
- diuretics +/- ACE inhibitors
Name the facial features of fragile x-syndrome and what gene is affected?
Long face
Large ears
Low set ears
Macrocephaly
FMR1
What tests do you want into leukaemia?
FBC
Blood film
LDH
Coagulation studies
Xrays:
- chest x-ray
- CT staging
Special tests:
- Bone marrow aspiration with aspiration
- Lumbar puncture
What are the poor prognostic factors for ALL?
<1 year, >10year
T cell differentiation
WCC >50
BCR ABL
What is prognosis of osteosarcoma?
75% at 5 years
30% if mets
What is treatment of rheumatic fever?
Penicillin V One of IM Benzyl-penicillin Aspirin \+/- Steroids for chorea
What are the complications of patent ductus arteriolas?
Reduce blood to extremities
- increased risk of NEC
- Hypotension
- Pulmonary congestion
- heart failure
What is a regular inhaler called and what can it be used with and what is another inhaler type which is purple?
Meter-dosed Inhaler
- can be used with spacer device
Diskus dry powder inhaler
- usually used >8 years old
When is the echocardiogram done in kawasaki disease?
Diagnosis, 14 days after and 6-8 weeks
What causes the mortality in congenital diaphragmatic hernias?
Pulmonary hypoplasia
What grades of salter-harris need discussed with ortho?
Grade III and IV
- risk of growth disturbance
How are you going to manage bronchiolitis?
Most cases can be managed in community with:
- paracetamol
- hydration
Admit if:
<94% sats
<50% feeds
Apnoea episodes
Management:
- get nasopharyngeal aspirates to confirm diagnosis to allow seclusion on wards
- Supportive oxygen if <94%
- Supportive feeds (try reducing amount and increase frequency first, then move to NG tube)
- nasal suctioning
**consider X-ray if you suspect hyperinflation or collapse
If more severe:
- Oxygen 15L mask
- IV fluids
- Inform PICU
*Ribavirin can be used for those with underlying conditions
What is the prognosis of bronchiolitis?
Symptoms usually peak on day 5.
A dry cough is usually left for several weeks
How long does a paediatric femoral fracture take to heal?
Age + 1 weeks
Most other fractures 2-3 weeks
Do you examine a child’s ears nose or throat with croup?
No.
What advice would you give parents for croup?
Usually worse at night
May worsen before it gets better
Worsening advice
5 year old with abdominal pain and vomiting, differentials:
Acute appendicitis Mesenteric Adenitis DKA UTI Male - testicular torsion
How does the pain of a hydatid compare to testicular torsion?
Slower onset