Neonatology

Question 1

What is babies circulating blood volume?

Answer 1

~80mL/kg

Question 2

At what point in embryology does ToF develop?

Answer 2

Embryonic

Question 3

When in the embryological stage does surfactant start to be produced?

Answer 3

From about 24 weeks in the saccular stage

Question 4

What is the most common type of ToF?

Answer 4

Type C - blind out pouching of the oesophagus with distal fistular connection

Question 5

Most common presentation for medullary sponge kidney?

Answer 5

Usually asymptomatic - present with stones, haematuria or UTI

Question 6

Bilious vomiting with absent bowel gases and NGT crossing the midline?

Answer 6

Duodenal atresia

Question 7

DiGeorge is due to 22q11 deletion diagnosed on FISH/Microarray - what is the embryology?

Answer 7

Abnormal development of 3rd and 4th pharyngeal pouch

Question 8

Classical ECG signs in tricuspid

Answer 8

LAD with Left side enlargement

Question 9

CCHS is associated with_______

Answer 9

Neuroblastoma and Hirschsprung disease

Question 10

CLICK (in murmur) means

Answer 10

VALVULAR PATHOLOGY

Question 11

Which surfactant protein deficiency is really bad?

Answer 11

Type B is really bad and they usually die. Death.

Type C is the other common one and they live

Question 12

Oxygen target aims in first 5 minutes of life

Answer 12

1 - 60% +
3 - 70% +
5 - 80% +

Question 13

Surfactant therapy increases the risk of _____

Answer 13

Pulmonary haemorrhage

Question 14

What three maternal antibodies is neonatal lupus seen with?

Answer 14

Anti-Ro
Anti-La
Anti-RNP

Question 15

Non-cardiac manifestations of Neonatal lupus typically resolve by __ months.

Treatment of skin manifestation can be ______

Treatment of cytopenias can be with _______

Answer 15

Resolve within 6 months

Skin manifestations - topical steroids

Cytopenia - treat with IVIG if significant