Motor Neurone Disease

Question 1

What is the most common and poor prognosis form of MND?

Answer 1

ALS - amyothrophic lateral sclerosis

Question 2

Bulbar onset starts with muscle wasting and poor control of mouth and tongue. The vast majority of this onset progresses into what form of MND?

Answer 2

ALS

Question 3

What is the average life expectancy after a diagnosis of MND?

How is MND diagnosed?

Answer 3

3 years

Clinical diagnosis

Question 4

What is MND?

Answer 4

Untreatable and rapidly progressive neurodegenerative syndrome

Question 5

Split the following symptoms into UMN and LMN symptoms:

• Increased tone
• Fasciculations
• Muscle wasting
• Weakness
• Spastic gait
• Slowed movement

Answer 5

UMN

• increased tone
• slowed movement
• spastic gait

LMN

• fasciculations
• muscle wasting
• weakness

Question 6

Only one drug can be used to manage MND and why do not many people end up taking it?

What is the name?

Answer 6

Only adds 3 months onto life - but right at the end when you are most disabled

Riluzole

Question 7

What kind of symptoms will ALS present with?

Answer 7

Mixed UMN and LMN

Most commonly present with muscle weakness/ hand or foot ‘not working properly’