Kartagener’s syndrome Flashcards
1
Q
Kartagener’s syndrome is also known as what?
A
primary ciliary dyskinesia
2
Q
using the surgical sieve what is the cause of Kartagener’s syndrome?
-1
A
genetic
3
Q
what is the basic pathophysiology of Kartagener’s syndrome?
basically what is wrong
A
Dynein motor protein is defective
4
Q
Associations with Kartagener’s syndrome?
-3
A
bronchiectasis, sinusitis, dextrocardia
5
Q
typical history of pt with Kartagener’s syndrome?
- 2 things
A
recurrent infections, chronic wet cough
6
Q
Kartagener’s syndrome pt now has bronchiectasis.
what medical Mx is there for this?
-2 things
A
Carbocisteine (mucolytic)
saline
