Idiopathic Pulmonary Fibrosis Flashcards

1
Q

Another name for Idiopathic Pulmonary Fibrosis?

A

Cryptogenic Fibrosing Alveolitis

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2
Q

What is Idiopathic Pulmonary Fibrosis?

A

This is pulmonary fibrosis that has no obvious underlying cause

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3
Q

What is Pulmonary Fibrosis?

A

This is scarring of the lung tissue. There is scarring and accumulation of fibrous connective tissue which causing a decline in lung function

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4
Q

Describe the pathophysiology of Idiopathic Pulmonary Fibrosis?

A

Cause is unknown

There is inflammatory cell infiltrate and lung tissue fibrosis

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5
Q

Risk factors for Idiopathic Pulmonary Fibrosis?

A

Smoking
Exposure to dust
Farming
Viral Infections

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6
Q

Symptoms of Idiopathic Pulmonary Fibrosis?

A

Exceptional Dyspnoea
Malaise
Weight Loss
Arthralgia

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7
Q

Signs of Idiopathic Pulmonary Fibrosis

A

Clubbing
Cyanosis
Fine End Inspiratory Crackles

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8
Q

Investigations in Idiopathic Pulmonary Fibrosis?

A

FBC - Increased CRP and increased Immunoglobulins
CXR - Decreased Lung Volume, Honeycombing, Bilateral Lower Zone Reticulo-Nodular Shadows
Spirometry - Restrictive

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9
Q

Complications of Pulmonary Fibrosis?

A

Respiratory Failure

Increases risk of Cancer

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10
Q

BUZZWORD?

A

Ground Glass Appearance

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11
Q

Treatment?

A

Supportive - Oxygen Therapy, Pulmonary Rehabilitation

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12
Q

Causes of Pulmonary Fibrosis Mnemoic?

A

BREASTI

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13
Q

Causes of Pulmonary Fibrosis Mnemonic + Answers

A
BREASTI 
Bleomycin
Radiation
Extrinsic Allergic Alveolitis
Asbestosis
Sarcoidosis
TB
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14
Q

B?

A

Bleomycin

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15
Q

R?

A

Radiation?

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16
Q

E?

A

Extrinsic Allergic Alveolitis

17
Q

A?

A

Asbestosis

18
Q

S?

A

Sarcoidosis

19
Q

T?

A

Tuberculosis

20
Q

Describe a lung function test for Pulmonary Fibrosis?

A

FEV1 is reduced
FVC is reduced
FEV1/FVC is normal or high

21
Q

When does this most commonly present?

A

50-60s