Idiopathic Pulmonary Fibrosis Flashcards
Another name for Idiopathic Pulmonary Fibrosis?
Cryptogenic Fibrosing Alveolitis
What is Idiopathic Pulmonary Fibrosis?
This is pulmonary fibrosis that has no obvious underlying cause
What is Pulmonary Fibrosis?
This is scarring of the lung tissue. There is scarring and accumulation of fibrous connective tissue which causing a decline in lung function
Describe the pathophysiology of Idiopathic Pulmonary Fibrosis?
Cause is unknown
There is inflammatory cell infiltrate and lung tissue fibrosis
Risk factors for Idiopathic Pulmonary Fibrosis?
Smoking
Exposure to dust
Farming
Viral Infections
Symptoms of Idiopathic Pulmonary Fibrosis?
Exceptional Dyspnoea
Malaise
Weight Loss
Arthralgia
Signs of Idiopathic Pulmonary Fibrosis
Clubbing
Cyanosis
Fine End Inspiratory Crackles
Investigations in Idiopathic Pulmonary Fibrosis?
FBC - Increased CRP and increased Immunoglobulins
CXR - Decreased Lung Volume, Honeycombing, Bilateral Lower Zone Reticulo-Nodular Shadows
Spirometry - Restrictive
Complications of Pulmonary Fibrosis?
Respiratory Failure
Increases risk of Cancer
BUZZWORD?
Ground Glass Appearance
Treatment?
Supportive - Oxygen Therapy, Pulmonary Rehabilitation
Causes of Pulmonary Fibrosis Mnemoic?
BREASTI
Causes of Pulmonary Fibrosis Mnemonic + Answers
BREASTI Bleomycin Radiation Extrinsic Allergic Alveolitis Asbestosis Sarcoidosis TB
B?
Bleomycin
R?
Radiation?