Congenital Heart Defect Flashcards
*____________ is the term describing a situation where the location of the heart is in the right side of the thorax, the left ventricle remaining in the normal position on the left, but lying anterior to the right ventricle.
Dextroversion
*Dextroposition - The heart is displaced to the right due to a mas (space occupying lesion) in the left chest
*L transposition is NOT Cyanotic.
T or F
T
Levo-TGA = acyanotic
*What are the 4 key factors of a TET. (Tetralogy of Fallot)
VSD
RVOT/Pulmonic obstruction
overriding aorta
RV hypertrophy
*D transposition is NOT Cyanotic.
T or F
F
Cyanotic
Dextra TGA
- 2 independent parallel circuits
- life dependent on PDA, PFOVSD
_ use Prostaglandin to maintain the shunts
*35% of patients with Truncus Arteriosus have DiGeorge Syndrome.
T or F
T
*Truncus Arteriosus associated findingds:
- Truncal Valve – Truncal valve is usually dysplastic with thickened and deformed leaflets i.e. bicuspid (Cusps usually range from 2-6)
- Coronary artery anomalies
- DiGeorge syndrome
- R. aortic arch
- interrupted aortic or coarctation
*List the six (6) steps in performing a pediatric echo using the “segmental approach.”
*Segmental Approach
atrial situs (disposition)
venous connections
aatrioventriular connections
ventricular morphology & position
ventricular connection
cardiac orientation (levo-, dextro-, mesocardia)
atrial situs (disposition)
atrioventricular junction
ventricular loop orientation
ventriculoarterial junction
position and relation of the great vessel
*TAPVR is the acronym for ___________ ___________ ________ ____________ ______.
total anomalous pulmonary venous return
*Dextrocardia or dextroversion may be associated with atrial-ventricular ____1____ and ventricular-arterial ____2____.
discordance
discordance
*List 4 key components of assessing a VSD with Echo.
Type of defect - location/size
AV valve structure (Common AV valve; Cleft mitral valve)
Chamber sizes and function (Increase length of apex to aortic valve forming the “gooseneck” deformity of the outflow tract; evaluate function of ventricles)
Pressure gradients(ASD;VSD;RVandPApressure)
Direction of shunt(s); Color and spectral Doppler (Pressure gradients; Valvular insufficiency
*List echo features of Hypoplastic Left Heart Syndrome.
reduced aortic annular size
small LV (less than 10mm)
distorted/absent MV
*You suspect that your patient may have an anomaly of IVC systemic venous return. You see: absence of hepatic segment with azygous vein continuation, absence of the abdominal segment with hemiazygous continuation, and the IVC is draining into the LA. What might you suspect?
interruption of IVC
*Initially patients with ASDs have left to right shunting due to right ventricular compliance being less that left ventricular compliance. However, prolonged shunting can result in the right to left shunting with elevated right sided pressures and Eisenmenger’s physiology (rare with ASDs).
T or F
T
*Abnormal development of endocardial cushions may result in a primum atrial septal defect and/or a membranous ventricular septal defect.
T or F
T
*List 3 types of VSDs.
Inlet
Outlet
muscular
membranous
*A patient who is diagnosed with situs inversus totalis has a heart that is structurally normal.
T or F
T
all the organs are in mirror position
*List 4 ways that color Doppler may assist you in the assessment of an ASD.
detect shunt direction
qualitate the size/location
evaluate mitral, tricuspid, and PV insufficiency
*An ASD may remain symptom free for many years.
T or F
T
*The PS -pulmonic stenosis- murmur is _______________.
crescendo-decrescendo