CHD - Adult Flashcards
What is situs solitus?
refers to the normal position of the thoracic and abdominal organs
normal orientation of heart called:
levocardia
Anomalies of Position Mirror Image Dextrocardia
Type 1
sistus inversus totalis
a condition in which the arrangement of the internal organs is a mirror image of normal anatomy.
Anomalies of Position Mirror Image Dextrocardia
Type 2
AV (atrial-ventricular) concordance
&
VA (ventricular-arterial) discordance
TGA (transposition of the great arteries) or Dextro-TGA/ d-TGA (dextro-loop occurs)
- rare
- creates 2 independent parallel circuits
- patients show cyanosis
- systemic flow: RA-RV-AO-body-RA
- venous flow: LA-LV-PA-lungs-LA
- rely on PDA, PFO, VSD to get oxygenated blood
- prostaglandin keeps shunt open
Anomalies of Position Mirror Image Dextrocardia
Type 3
AV (atrial-ventricular) discordance
&
VA (ventricular-arterial) discordance
Atrioventricular and ventriculoarterial discordance, also known as congenitally corrected transposition of the great arteries: Levo-TGA/l TGA/Corrected TGA
- ventricles are transposed (RV in LV position becoming arterial ventricle & LV in RV position becoming venous ventricle)
- If no other defects present, heart function normally for 15-20 years
- eventually systemic ventricle (RV in LV position) will fail
Anomalies of Position Mirror Image Dextrocardia
Type 4
AV (atrial-ventricular) discordance
&
VA (ventricular-arterial) concordance
- rare
- inverted heart
- normally related great vessels
Most common congenital anomaly involving the _________
systemic veins
Anomalies of Venous Return:
Most common form is the _____drains into the RA via the _______
*Appears as a dilated coronary sinus on PLAX and A4C with inferior angulation
left SVC
coronary sinus
*Left SVC draining into LA occurs less often
SVC systemic venous return
Contrast injection into the _____will opacify the coronary sinus before the RA and RV. If the same injection leads to left atrial opacification, abnormal drainage of the vena cava is present.
left arm
Anomalies of Venous Return:
_______ occurs when interruption of the IVC;
- Absence of hepatic segment with azygous vein continuation
- Absence of the abdominal segment with hemiazygous continuation
- The IVC draining into the LA
occur
Aanomalies of IVC systemic venous return
_______ is a condition in which all four of the pulmonary veins are abnormally connected to the right atrium instead of the left atrium. This allows blood high in oxygen to enter the right side of the heart. Blood high in oxygen flows across an ASD, to the left ventricle, allowing some blood with oxygen to reach the body. Without the ASD, blood high in oxygen would not be able to reach the body.
occurs when absence of the right SVC & absence of hepatic segment of IVC
- blood flows from the IVC to the azygous vein to the left AVC to LA
- hepatic veins drains into the LA
- common atrium
Total anomalous pulmonary venous return (TAPVR)
or
Total anomalous pulmonary venous drainage (TAPVD)
What is TAPVR?
Total anomalous pulmonary venous return (TAPVR) is a birth defect of the heart.
abnormal pulmonary veins connection which brings oxygenated blood back to RA instead of LA.
Normally, oxygen-rich blood goes from the lungs to LA and then flows through the body. In TAPVR, an abnormal connection of veins sends blood through the RA instead, where it mixes with oxygen-poor blood. As a result, blood flowing to the body doesn’t have enough oxygen.
types of TAPVR
- supracardiac - PV drains into SVC
- intracardiac - PV drains into CS
- infracardiac - PV drains into SVC
*interrogate and look for confluence of all PV for echo
Anomalies of the Atria:
PFO found in approximately ____ % of population located in the _______
20-25
fossa ovalis
Anomalies of the Atria:
major types of ASD
- ostium primum - fuse with endocardial cushions
- ostium secundum - most common
- sinus venosus (inferiro/superior) - least common *also called: SVC (superior vena caval) septal defect/IVC (inferior vena caval) septal defect
- coronary sinus - rare
- common atrium
- atrial septal defect in the septum intermidium
What type of ASD?
- Second most common type of ASD
- Failure of septum primum to fuse with the endocardial cushions
- Located in the inferior atrial septum
- associated anomalies include malformation of MV
ostium primum
What type of ASD?
- Most common type of ASD (70%)
- Located in the midportion of the atrial septum.*
- Perforations in the interatrial septum
- Excessive resorption of septum primum
ostium scundum
What type of ASD?
- Least common form (10%)
- Also known as superior vena caval & superior vena caval
- not properly incorporated into the RA.
- Located in the superior and posterior portion of the atrial septum near the junction of SVC/IVC
- Frequently associated with _partial_ anomalous pulmonary venous return
sinus venosus ASD
What type of ASD?
- Rare
- Results from a lack of formation of the atriosinus venosus fold
- Original large communication between atria and sinus venosus is preserved
- Located between the inferior limbic septum, pars atrioventricularis of membranous septum and IVC orifice close to coronary sinus
coronary sinus
What type of ASD?
absence or near absence of the IAS resulting in ine common atrial chamber (rare)
common atrium
What type of ASD?
- rare
- Defect occurs as a true persistence of the embryonic foramen primum
- Located between the limbic septum, pars atrioventricularis of the membranous septum and ccoronaray sinus
ASD in the septum intermedium
Initially left to right shunting due to right ventricular compliance being less that left ventricular compliance. Prolonged shunting can result in the ____shunting with elevated right sided pressures and _____physiology (rare with ASDs)
- right to left*
- Eisenmenger’s*
Signs and symptoms (clinical presentation) of ASD
- asymptomatic for many years
- SOB on exertion
- recurrent respiratory infections
- Afib
- diastolic murmur via TV for a large shunt
ASD echo indication
- enlarged RA/RV
- D shape LV
- elevated RV/RA pressure
- PHTN
ASD Doppler Assessment
From a low parasternal 4ch, apical 4ch, subcostal 4ch view, and subcostal short-axis view, place color-flow map on ____ gate in atrial septum to look for ______ turbulence
- PW*
- late systolic early diastolic*
Qp:Qs ratio
normal ration should be
1:1
Qp:Qs ratio
ratio > 1.0 indicates
left to right shunt
Qp:Qs ratio
ratio < 1.0 indicates
right to left
PA pressure estimate from TR Doppler signal
peak <30 mmHg indicates
normal
*note: Normal resting values are usually defined as a peak TR gradient of 2.8 to 2.9 m/s or a peak systolic pressure of 35 to 36 mmHg, assuming an RA pressure of 3 to 5 mmHg.
PA pressure estimate from TR Doppler signal
peak 40-70 mmHg indicates
moderate
PA pressure estimate from TR Doppler signal
mean ≥40 mmHg indicates
severe
osteum Secundum defects are best visualized in the _______
subcostal 4ch