CF- Nutrition/GI Manifestations and Treatments

Question 1

BMI goal for kids with CF

Answer 1

≥50th percentile

Question 2

BMI goal for men with CF

Answer 2

≥23

Question 3

BMI goal for women with CF

Answer 3

≥22

Question 4

CF diet

Answer 4

Moderate fat, high protein, high caloric

Question 5

Enteral feedings may be useful for what kinds of CF patients?

Answer 5

children falling off the growth curve, adults not gaining/maintaining weight

Question 6

Creon dosing for infants

Answer 6

2000-5000 units/120ml formula

Question 7

Creon dosing for children ≤4 years

Answer 7

1000 units/kg with meals, 1/2 dose with snacks sprinkled over applesauce

Question 8

Creon dosing for children >4 and adults

Answer 8

400-500 units/kg with meals and 1/2 dose with snacks

Children up to 8 years old should get it sprinkled over applesauce

Question 9

How to choose the right Creon capsule dose

Answer 9

Pick a dose that will allow a full capsule dose at meals and snacktime

Decrease the dose if the patient’s symptoms are improving or have side effects

Increase the dose if the patient has poor weight gain, increased number of fatty stools, bloating

Question 10

ADEK dosing for <12 months

Answer 10

1ml PO QD

Question 11

ADEK dosing for 1-3 years old

Answer 11

2ml PO QD

Question 12

ADEK dosing for 4-10 years old

Answer 12

1 tab PO QD

Question 13

ADEK dosing for >10 years old

Answer 13

2 tabs PO QD

Question 14

Vitamin D supplement for ages 1-11

Answer 14

1000 IU QD

Question 15

Vit D supplement for ages >11

Answer 15

2000 IU QD

Question 16

Vit D dosing if level is <30ng/ml in age ≤5

Answer 16

50,000 IU MWF x1 month

Question 17

Vit D dosing if level is <30ng/ml in age >5

Answer 17

50,000 IU QD x1 month

Question 18

Vittamin K dosing during ABX treatment

Answer 18

5mg PO BIW

Question 19

Supplement for poor weight gain

Answer 19

Zinc sulfate- 1mg/kg/day DIV BID

Question 20

Other supplement

Answer 20

Ferrous sulfate