Week 3 - E - Paediatric hip prbolems - Development dysplasia, Transient synovitis, Perthe's disease, S.U.F.E Flashcards

1
Q

What is developmental dysplasia of the hip?

A

Developmental dysplasia of the hip is a condition where there is dislocation or subluxation of the femoral head during the perinatal period which affects the subsequent development of the hip joint

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2
Q

Which hip is DDH more common in? Which sex is DDH more common in? And can it occur in both hips?

A

DDH is more common in the left hip DDH is more common in female babies and in 20% of cases is bilateral

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3
Q

What are the different risk factors for developmental dysplasia of the hip?

A

Risk factors include Positive family history of DDH Breech presentation First born babies DOwn’s syndrome Other congenital disorders eg talipes

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4
Q

If left untreated, what can the developmental dysplasia of the hip cause to the hip joint? What is therefore more likely to occur at a young age?

A

If left untreated, the acetabulum is very shallow and in more severe cases a false acetabulum occurs proximal to the original one with a shortened limb Severe arthritis due to a reduced contact area can occur at a young age and gait / mobility may be severely affected

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5
Q

What are the presenting signs of a DDH? What are the examinations procedures carried out to test for DDH after birth?

A

Signs of DDH include Shortening of the limb Asymmetric groin / thigh skin creases Click or clunk on the Ortalani and Barlow test

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6
Q

How are the Ortalani and Barlow tests carried out?

A

Ortlani test is where you attempt to reduce an already dislocated hip with abduction and anterior dispacement (Ortalni for already Out) Barlow test - dislocataBle hip - attempt to disclocate the hip with flexion and posterior displacement

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7
Q

If the patient has an unstable hip with a positive Ortalani test or Barlow test, what mode of investigation is carried out? When does the choice of investigation change and why?

A

Ultrasound scan is the imaging of choice in babies up to the age of 4-6 months After this xrays are the investigation of choice - have to wait this long as the femoral head epiphyses is unossified until around 4-6 months

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8
Q

What is used as the treatment of developmental dysplasia of the hip?

A

A special harness known as a pavlik harness is used which keeps the hips in comfortable flexion and abduction thus maintaining reduction

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9
Q

What can over-flexing and abduction of the hip result in DDH? - this is the worst possible outcome of treatment

A

Over-flexion and abduction of the hip in the Pavlik Harness can result in avascular necrosis of the hip

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10
Q

How long is the pavlik harness used for?

A

Pavlik harness is used full time for around 6 weeks, then part-time for another 6 weeks once the hip is confirmed to be stable It can be used for up to 4-6 months

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11
Q

For children with persistent dislocation over 18 months old, what is likely to be required as treatment?

A

For children with persistent dislocation over 18 months old open reduction is much more likely to be required and the acetabulum is likely to be very shallow by this stage They may also need femoral / pelvic osteotomies to maintain joint stability

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12
Q

What is transient synovitis of the hip?

A

Transient synovitis of the hip as its name suggest is self-limiting inflammation of the synovium of the hip joint - it is the commonest cause of hip pain in childhood

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13
Q

What age group / sex does transient synovitis of the hip tend to affect and what does it typically occur after?

A

Transient synovitis of the hip tends to affect boys aged between 2 and 10 years old It typically occurs after an upper respiratory tract infection (usually viral) although sometimes no cause is found

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14
Q

What is the most important pathology that you must rule out when considering transient synovitis of the hip?

A

YOU MUST RULE OUT SEPTIC ARTHRITIS Take bloods - WBC, ESR/CRP should all be within normal range in transient synovitis of the hip

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15
Q

What other conditions should be considered for causing hip pain?

A

Also consider * Perthe’s diseasee * SUFE (slipped upper femoral epiphyses) * Juvenile idiopathic arthritis * Rheumatoid arthritis Xray may be useful

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16
Q

What are the presenting features of transient synovitis of the hip?

A

Presentation is with a limp or reluctance to weight bear on the affected side * Range of motion may be restricted (not as much as pain or loss of motion as septic arthritis) * Child may have a low grade fever but is not systemically unwell or septic

17
Q

Once a more serious cause of hip pain has been excluded (bloods, radiographs), what is the treatment of transient synovitis of the hip?

A

Short course of NSAIDs and rest Pain generally resolves within a few weeks If there is no resolution, another causes of hip pain such as juvenile idiopathic arthritis or Perthe’s should be sought

18
Q

What is Perthe’s disease also known as? What is Perthe’s disease?

A

Perthe’s disease (aka Legg-Calve-Perthe disease) is an idiopathic osteochondritis of the femoral head (a type of compression osteochondritis)

19
Q

What age group and sex is affected by Perthe’s disease?

A

Perthe’s disease is especially common in boys of short stature aged 4-9 years old

20
Q

What happens to the femoral head in Perthe’s disease?

A

The femoral head transiently loses its blood supply resulting in necrosis which may lead to femoral head collapse and/or racture Subsequent remodelling occurs however the shape of the femoral head and congruence of the joint can vary

21
Q

What are the presenting features of Perthe’s disease? Are causes normally unilateral or bilateral?

A

Affected children typically present with pain and a limp Most cases are unilateral and bilateral cases may represent an unerlying skeletal dysplasia or thrombophilia

22
Q

What is the first clinical sign on examination in patients with Perthe’s disease? What is this followed by?

A

Loss of internal rotation (and abduction) is usually the first clinical sign followed by loss of abduction and later on a positive Trendellenburg test from gluteal weakness Gluteus medius and minimus - cause internal rotation and abduction of the hip joint

23
Q

How is Perthe’s disease diagnosed and how is it treated?

A

Perthe’s disease is diagnosed typically by carrying out bilateral hip xrays- may see femoral head collapse and fragmentation No specific treatment - avoid exercise and rest (50% of cases do well)

24
Q

What is SUFE? What is the typical patient that is affected?

A

SUFE stands for slipped upper femoral epiphyses It is a condition mainly affected overweight pre-pubertal adolescent boys where the femoral head epiphyses slips inferiorly in relation to the femoral neck

25
Q

Why does the femoral head epiphyses slip in SUFE? What conditions may predispose to SUFE?

A

In the condition, the growth plate (physis) is not strong enough to support body weight and the femoral epiphysis slips due to the strain Hypothyroidism or renal disease may predispose to SUFE

26
Q

What are the presenting symptoms of SUFE?

A

Presenting symptoms include pain felt in the groin - like in other hip pathology, also with a limp However patients may also/only present with pain in the knee due to the obturator nerve supplying both the hip and knee joint

27
Q

What is the predominant clinical sign of SUFE? What xray view is important to obtain for this condition?

A

Loss of internal rotation of the hip is the predominant clinical sign. Xray changes may be subtle and a lateral view must be obtained to detect mild degrees of slip.

28
Q

What is the treatment of SUFE?

A

The treatment of SUFE is urgent surgery to pin the femoral head to prevent further slippage - internal fixation: typically a single cannulated screw placed in the center of the epiphysis The greater the degree of slip, the worse the prognosis. Some cases may require hip replacement in adolescence or early adulthood