Rheumatology

Question 1

What i s the MCC of acquired heart dz in peds?

Answer 1

Kawasaki dz

Question 2

Signs/sx’s of Kawasaki dz?

Answer 2

Conjunctivitis, Rash, Adenopathy, Strawberry tongue, Hands/feet swollen, Fever 5+ days, up to age 7, mucosal changes, skin desquamation, coronary aneurysms,

Question 3

What is the tx for Kawasaki dz?

Answer 3

ADMIT! EKG/echocardiogram, IVIG 2g/kg over 10-12hrs, high dose ASA, low dose ASA

Question 4

What is systemic lupus erythematosus (SLE)?

Answer 4

multi system inflammatory dz from immune complex deposits in tissues, more common in non-whites, less common in young kids

Question 5

Signs and sx’s of SLE?

Answer 5

malar rash, oral ulcers, abd pain, arthritis, low blood counts, hematuria, proteinuria, HTN, HA, discoid lesions, CVA, atherosclerosis, photosensitivity, seizures, high ANA

Question 6

Tx for SLE?

Answer 6

corticosteroids, methotrexate, cyclophosphamide, azathiprine, hydroxychloroquine

Question 7

What is the most prevalent chronic rheumatologic dz in peds?

Answer 7

juvenile rheumatoid arthritis (juvenile idiopathic arthritis), peaking at 1-3 and 8-12yo

Question 8

What are s/sx’s of systemic onset JIA?

Answer 8

arthralgia, pink macular rash, HSM, LAD, fever, serositis, pleural/pericardial effusion

Question 9

What are s/sx’s of pauciarticular JIA?

Answer 9

lg jt arthritis, uveitis, less than 5 joints involved, ANA +, RF -, 90% remission

Question 10

What are s/sx’s of polyarticular JIA?

Answer 10

> 5 jts, symmetrical involvement, uveitis, malaise, anemia, fever, rheumatoid +

Question 11

Sign/sx’s of dermatomyositis?

Answer 11

proximal m. weakness, m tenderness, absent DTRs, heliotrope rash on eyelids, Gottron’s papules on extensor surfaces (scaly red lesions)

Question 12

What is a complication of untreated uveitis?

Answer 12

blindness